are a group of rare disorders characterized by metabolic pathway abnormalities. One such disorder is Maple Syrup Urine Disease (MSUD) otherwise known as Branched-chain Ketoaciduria, a dangerous condition in which over saturation of amino acids in the blood can lead to toxicity progressing to encephalopathy, neurodegeneration, coma or respiratory failure (Haldeman-Englert, 2015). MSUD results from a malfunction of the branched-chain alpha-ketoacid dehydrogenase complex (BCKD) (Kniffin, 2013). This complex produces enzymes necessary for the proper breakdown of common amino acids such as valine, leucine, and isoleucine, are found most abundantly in protein rich foods (Strauss et. al, 2013). When the aforementioned amino acids are not broken down they remain in the blood along with their keto acids leading to acidemia (Strauss et. al, 2013). As discussed by the National Organization for Rare Disorders (NORD) MSUD is caused by an autosomal recessive mutation, indicating that the…
Page 1 Once upon a time in a kitchen not so far away, there lived in a small cottage made of milk and honey and all things yummy, Patty Pancake, Mommy Muffin and Daddy Doughnut. Page 2 Patty Pancake was so excited to begin her first day of school at Maple Syrup elementary. Telling Mommy Muffin and Daddy Doughnut about all of the friends she would meet. Page 3 Mrs. Danish, her teacher introduced Patty Pancake to her new classmates. “Good morning class, a new student has joined us today. Please…
1.) How does the maple syrup industry reflect what we learned in class about cartels? Describe what makes FPAQs maple syrup so special (i.e., uniquely differentiated) FPAQs maple syrup is special because there are cartels of maple syrup that set the prices and negotiate with buyers. It is uniquely different because of the different seasons of maple syrup collection. With this, there is a stable market to sell maple syrup. Reference the definition of cartels and joint-profit maximization As…
Suger maple(Acer saccharum) Aceraceae/ Maple family sometimes called rock maple or hard maple, it is one of the largest hardwoods that is wide spreaded in western Canada. Sugar maple is common associtated with those common types: Acer negundo,manitoba maple Acer ginnala,amur maple Acer sacharrinum,silver maple Tree with overall up to 35 m tall, long straight trunk, usually branch-free for 2/3rds of its height. Leaves: Simple leaves, oppositely arranged and they’re flat, with three or five…
Fundamentals of Biochemistry in the Biotech Industry Maple Syrup Urine Disease: A Sweet Scented Killer Maple Syrup Urine Disease (MSUD) is a rare, potentially deadly disorder where the body cannot break down the three branched- chained amino acids (BCCA): leucine, isoleucine and valine. These amino acids are used to build proteins and when they are not being used they can be broken down and recycled in the cell. The complex that breaks these amino acids down is called BCKD (branched-chain…
Word Count: 1372 THE ‘B’ GRADE Matthew S. Tapper loved the taste of maple syrup. He had no clue how it was made, and would salivate whenever he saw the ‘B’ grade pasted on a plastic half pint jug. (Backstory: Not too many years back and for most of his millennial life when money flowed, the good Mr. Tapper went through gallon jugs of ‘B’ grade faster than the 4 or 5 at full throttle between 59th and 86th.) Deep into his man purse he would dive for the errant coins that vacationed way…
Case Study #1: When you should put maple syrup on Pizza Summary Coming from Chicago Illinois Rafael Esposito was inspired to create something different concerning Pizza. Through years of testing and development, Raphael worked to create a breakfast pizza with a waffle crust he named the Pizzafle. The Pizzafle is unique in its design because it can be eaten and carried around like an ice cream cone. Upon the creation of the Pizzafle. Mr. Esposito moved his family and the business to St Augustine…
well when worn with a strap without tilting toward the headstock or the body. The larger or thicker bodies, especially those made of heavier woods, can be very heavy and tiring to play. Guitar Body Woods The look of each piece of wood is unique; even within one tree species, pieces vary from one to the next in grain pattern, color weight, and density. The sonic properties of different woods and their different and densities, vary dramatically. Every once sustained well and have a brighter,…
no times I could sit up on my hospital bed and ate my meals with no helps. After I was strong enough to walked to the bathrooms right down the hall, I begged to took me down to the park right next to the hospital. I’ve never been a friend of Mother Nature all these years I’m alive. But this time I was willing to make her my lover. The chirpings of the birds hidden in the trees were the best songs I ever heard. The sunlight escaped through the tree leaves and shone on my hair; killing the…
Donald, took up where his father left off, mastering a method of unethical abuses throughout his business practices. Regarding verse 3:28, “Do not say to your neighbor, ‘Go, and come back, and tomorrow I will give it,’ when you have it with you.” Trump has a long history of making financial promises and failing to “pony up”. The veterans fund raiser is a classic example where the media had to hound him for the money. When they did, they were of course castigated as sleazes by Trump. He has…