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16 Cards in this Set
- Front
- Back
Degradation of stored glycogen |
CYTOSOL |
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The degradation of stored glycogen is triggered by: |
LOW BLOOD GLUCOSE LEVELS |
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Why glycogenolysis occurs? |
1. When organism needs energy 2. During muscular exercise |
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TYPE 0 |
Glycogen synthase |
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TYPE 1a VON GIERKE DISEASE |
Glucose 6-phosphatase |
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TYPE Ib |
Endoplasmic reticulum glucose 6-phosphate transporter |
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TYPE II POMPE DISEASE |
Acid maltase |
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TYPE IIIa LIMIT DEXTRINOSIS, FORBE, OR CORI |
Liver and muscle debranching enzyme |
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TYPE IIIb LIMIT DEXTRINOSIS |
Liver debranching enzyme |
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TYPE IV AMYLOPECTINOSIS, ANDERSEN DISEASE |
Branching enzyme |
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TYPE V MYOPHOSPHORYLASE DEFICIENCY, MCCARDLE SYNDROME |
MUSCLE PHOSPHORYLASE |
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TYPE VI HERS DISEASE |
Liver Phosphorylase |
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TYPE VII TAURI DISEASE |
Muscle and erythrocyte phosphofructokinase I |
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TYPE VIII |
Liver phosphorylase kinase |
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TYPE IX |
liver and muscle phosphorylase kinase |
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TYPE X |
C-AMP dependent protein kinase A |