Reading...
Play button
Play button
Use LEFT and RIGHT arrow keys to navigate between flashcards;
Use UP and DOWN arrow keys to flip the card;
H to show hint;
A reads text to speech;
18 Cards in this Set
- Front
- Back
|
glucose + glucose?
|
maltose
alpha 1,4 |
|
|
galactose + glucose?
|
lactose
beta 1,4 |
|
|
glucose + fructose?
|
sucrose
alpha 1,2 |
|
|
glucoses with amino groups makes up which polysaccharide?
|
chitin
|
|
|
Which polysaccharides are made up of glucose only (3)?
|
starch
glycogen cellulose |
|
|
What is the enzyme defect in fructosuria?
|
fructokinase
|
|
|
Which saccharide disorder results in fructose in the urine but is benign?
|
fructosuria
|
|
|
What is the enzyme defect in fructose intolerance?
|
aldolase B
|
|
|
In which saccharide disorder does fructose-1-P build up in the liver and kidney causing renal and liver failure?
|
fructose intolerance
|
|
|
Which saccharide disorder also causes a backup iin glycolysis resulting in dangerous hypoglycemia, especially between meals?
|
Fructose intolerance
|
|
|
When Glucose-6-PO4 accumulates what processes are shut down?
|
glycogenolysis and gluconeogenesis
|
|
|
Which saccharide disorder results in flatus, bloating, boborygmi, and diarrhea due to increased lactose within the intestinal lumen?
|
lactose intolerance
|
|
|
what enzyme defect is present in lactose intolerance?
|
lactase
|
|
|
How does the lactose tolerance test work?
|
give pt 50 g lactose see if they get symptoms w/i 20-30 min; have them come back and give 50 g glucose and get no S&S but do get an increase in serum glucose = (+) TEST
|
|
|
Which saccharide disorder results in MR, physical stunting, liver failure?
|
galactosuria
|
|
|
what is the defective enzyme in galactosuria?
|
galactose-1-PO4 uridylyl transferase
|
|
|
What may develop in a fetus in utero whose mother is galactosemic and uncontrolled?
|
cataracts
|
|
|
Within a few weeks after birth and after being fed milk, infant becomes anorexic, vomits, stops growing and becomes icteric; what is the likely diagnosis?
|
galactosuria
|
