Ravilya_Pediatrics_ Cardiology_Ps

Front 1

Pulmonary stenosis (PS) associated with disease

Back 1

Pulmonary stenosis (PS) associated with disease: Noonan syndrome, neurofibromatosis. Pulmonary valve dysplasia is noted in Noonan syndrome.

Front 2

Most common type of pulmonic stenosis:

Back 2

Most common type of pulmonic stenosis:(important)valvular stenosis

Front 3

Most common complication of pulmonic stenosis:

Back 3

Most common complication of pulmonic stenosis: congestive cardiac failure. It occurs in severe cases within first month of life. In severe PS, cyanosis occurs in infancy due to right-to-left shunt through foramen ovale. Infective endocarditis can occur, but not common in childhood

Front 4

Name one congenital heart disease where child is well-developed and healthy:

Back 4

Name one congenital heart disease where child is well-developed and healthy: pulmonic stenosis. (Most cardiac diseases are associated with poor growth and development.)

Front 5

A case presentation of PS:

Key words:

Back 5

A case presentation of PS:
infant shows signs of cyanosis,d yspnea,and right ventricular failure,but is well-developed and well-nourished; examination reveals systolic ejection murmur heard best during expiration, split 2nd heart sound. (A critical pulmonic stenosis indicates right-to-left shunt through a patent foramen ovale, cyanosis markedly decreased right ventricular compliance, and right ventricular failure.)

MOST LIKELY DIAGNOSIS: pulmonic stenosis.

CHEST X-RAY: diminished pulmonary circulation, cardiomegaly. EKG: right ventricular hypertrophy. DIAGNOSIS CONFIRMED BY: echocardiogram.
TREATMENT:
(a)
Mild and asymptomatic patient can lead normal life,no surgery necessary.
(b)
Moderate-to-severe with symptomatic patient:

TREATMENT OF CHOICE: balloon pulmonary valvuloplasty is initial treatment of choice. Newborn with critical
stenosis needs balloon valvuloplasty or surgical valvotomy as soon as possible.
Key words: well-developed and wen-nourished, systolic ejection murmur heard best during expiration, split 2ndheart sound