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506 Cards in this Set
- Front
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conduct disorder
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has a problem with everybody
and yonger than 18 years |
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macrocytin aner with congential pure red blood cell anemai
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Diamond blackfan sndromw
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21 hydrolasxes defecienty can present as how
AR enzymes |
adrenal insuffiency
hyponateria hyperkale and metabloci acdiosisis |
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breat milk
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give vit K
will have PTT and Pt elevation |
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hemipariasis after seizure
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todds
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rx to DTap
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serious CNS problem within 7 dyas anaplyactic reaction
DT should be sustitued acetaminophen helps reduce the discomfort |
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hyperinflation gournd glass apearanc staccoto cough
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chlamydia trachomatis
history of eye discarge low grade or no fever 6 weeks to 6 months |
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what are the labs for systemic usualy
|
RF- and ANA-
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high spiking fevers
salamon colored rash heptospleonmegaly plerurit and percardits |
systemic jra
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sits unsupporte rakes at pellt
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6 months
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h influeze and n emingits what do you give close contacts
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rifampin
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RSV dx
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Elisa ish highly senstive and specific
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hold head up
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3 montsh
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neonate that has jitter tremors and excitabiliry
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Infants of diabit mother
baby produce lost of insuline |
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neonatate with coarse jittera and very irritable high pitche cry
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herion and methadone
heroin 48 hours and methodone everaa weeks |
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tx for older menigitis
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ceftriaxone and vancomycin
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ground gallas apperasce of lungs
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RDS
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LETHARY POOF RDDIGN AND HIGH PTICHED CRY HYPERTONCITY ADN SEZIURES
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kERNICTUERS
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neonate start bleedin
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deficien in vit k
phenobarbital |
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fever knee red warm and swollen
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mcc is staph aureus
do arthrocentisic |
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5 days of ages purulen conjuctiva
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gongcocal
tx with ceftriazxoe |
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paralysis f hand ipsilater horner
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klumpke
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Reye
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encehpalopathy with fatty degeneration of the liver
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blood and wbc in stool
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celica dx salmonella shigell amebisais rotaviruse
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sel mutilation choreoatheotiss spasticyt retardation gouty arthirtis and reanl calculi
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lesch nyhan
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tx of lesch cyhan
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allopurinol
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seizures catarcat hypoglycemia jaundic vomiting
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galactose 1 urdiyl transferase
increase in E coli |
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CNS and heart problems
Wide QRS |
Tricycli antiderpressants
|
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what can a kid get from acetaminophen
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fluminat hepatic necrosis
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tx of rmsf child less than 8
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chrophenicol
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what is rapidly depleted in acetamniophen
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gluatthinoes is rapdily depleted
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decearces visual acityon in a kid with nerufibromations
asymmetric nytagmus |
optic gliomas
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faliure of upawar gavze
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pineloma
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hydrocephalus and myuelomengocele
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arnold chirar syndrome
type 2 |
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demyelinat of CNS adreanl insufficenty metanl deterioaton ahphas aprxia and dysarthria
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adrenolekodystropyy
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tx of Tricyclic antidepressants
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Sodium Bicarbonate presnt dyshythmias
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drawfism
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type 2 collagen
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hemihypertropy macroglossia vesomegaly
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beckwith wiedemann syndrome
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copies squanre
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4 years
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bone pain only at night in 7 years
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growing pains
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what does pauciarticualr requires
|
slit lamp exam
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Crash and burn for kawa
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conjuncitiits
Rash adenophaty strawberry tongue hands and fet burn |
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cataract in metbolism problem
in neonate |
galactosemia
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spianl musclue atyplohy
contrinuatio of programemed cell death sparing of the extraocular musle adn spincter is characteri |
werding hoffman
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chlamydia conjuctivie
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tx with erytomycin
topical and systemically |
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mcc of retrophyrgeal absceess and pertionsillar abscess
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group A strept
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< 6 months post tussive emeesis and apnea
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pertursis elevated wbc adn lymphocytosis >70%
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transpostion OF ARTETITES
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most comon congentia hear disease in the fist 24 h of life
tx with prostalgadin e1 KEEP PDA OPEN HIGH YEILD |
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term baby tachpnea and hypoxia patch infiltrate
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Meconium aspiration syndrome
tx mechanical ventilati ntiic oxid adn ECMO |
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complication fo Vesicourteral relux
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renal scarring
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localsize tendernes of tibial tuberecle
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osgood schlatter dz
active boys around puberty |
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gross hematureia edeam hpertension and reanl insufficiey
c3 is low |
posttrep glomerlneprtis
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what is low in cow milk when do you use it
|
low iron and copper anemia
high protien cuasing renal damage use of on year of age |
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what shortens the commubiablty
of pertussis |
ertyromycin and give close contact should ertyhromcyine
14 days |
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tx of OM
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amoxicllin
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mcc cuase of conjuctivis in first 24 hours
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chemical
|
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arthrits larger joints
asymemetric |
pausciarticualr high risk for eye involvemen
iridocyclitis |
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Rubella and cardia
Tuners |
rubellA PDA
tuners coarctaiton low femoral pulse |
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toxo
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intrcranical calcifications
dx by IgM tx spiramycin and pyrimethamine and sulfonamide for mother Steroids for choriretinits |
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CMV
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petechia jaundice hearing lss and periventricualr calcifications
dx culture and PCR |
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rash on face then trunk
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mealses and rubella
rubllea will have some lymphadenophaty |
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Shock hepatorenal failur metabolic acidos
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Iron posiniong
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what is recommend for measles
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vit A
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menigitis <3 and <3
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group B L monocytogenes Ecoli
N memingits S pnemone and h influeza |
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tx for infantile spams
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ACTH and prednisone
bc the crh is overproduced |
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headache syncope tachycardi nasue vomitng tachpena
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CO
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EEG for infantile spams
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hypsarrhythmia
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age of infatile spams
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4-8 months
|
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complex febrle seizure has an increase in what
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increase incideine of epliisyp 10%
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HUS Hemo
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high wbc low platlets
low hb helmelt and burr cells |
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complex is focal or generlaized
|
focal
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leading cause of blindness in kids
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trochoma
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dx and tx of trochma
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lymphod follicles in corena
tx erytomycin |
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tx of kawaskai
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ivg and hig does aspirin
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what is the mneominc for kawasaki
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My Heart
mucos H Eyes conjuctiva injection Adenitsi lymp Rash Temp |
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what can be shown in shanken baby syndrome
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rentinal hemorrages
subdural hematoma |
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what is messed in in Fri-Ataxia
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frataxin mitochondria protien expanded GAA triplet
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pres of Friedric ataxin
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dysarthirc speed and nystagumne
|
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physical exam of frid atsxa
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absent deep tendon reflex high arch foot and hammertoes kyphoscolosis
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what type of tumor is rhabdomyosarco
|
straite muscle
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rahbodmyso in vaginal
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sarcoma botryoies grpaleike masss
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where can rhabdo apper
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anywhere in nasophyare trucnk
bladder do ct for nose and head cytstouerthrogram for bladder |
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conunctivis that cuase pneomani in newborn
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chylamdiea tx with eryotpmycin
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mcc cuase of blood in stool of newborn
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swallowed maternal blood
use apt test to distingish the tow |
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1st thing to do in wilms
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ultrasound
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prestentation of wilms
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HTN hematuria
genitourinary tract hemihypertrypo anirida |
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dx and tx of wilms
|
ultrasound
ct and biposy can metatstaix surgery readiothrerapy and chemotherapy |
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Di geogers syndromw
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CATCH 22
Cardia anomales Abnoraml facies Tyhmic hypoplas Celf palate Hypocalcemia chromsosme 22 |
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microcephaly
short aplerbral fissure maxillary hypoplasi ashort nose smotth philturm and smooth uper lip |
fetal alchol syndorme
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Ataxia telangiectas increase of what
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Hodgkin leukemai and sarcoma
|
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Ataxia Telani have increase infections bc
|
low or absent IgA and IgE
t cell probalesm |
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parder willie
|
hypotonia hypogondaism hypomentai and obestiy
|
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forbrain abonmailetie and MR
midline and midlien clefts scalp defects holprosecephaly |
Patauam 13
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hands held in typical clenchin g psture rocker bottom feet and hammertoes
low set ears VSD |
edwards 18 elction agea
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increase in Downs
|
doudenal atreai endocardia cushin defect ataloataxia instabily lefukema and thyrodi dz
hisprugs |
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mcc of MR in boys
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Fragile X large testicla prominat jaw large years large head
|
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tx of klinefelter
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teststerone repalcement
|
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mcc of infertily in males
|
klinefelter syndrome
|
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wiskott aldrich
|
WATER
low IgM IgA high thrompcytopenia Excezm recurrect infections |
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limping in newborm to 3 years
|
DDH associated with breech psotion and troticollis
tx containment is the key |
|
|
Rubllea in infact
|
Deafness Blindness
|
|
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a vascualr necrosis of femaral head
|
legg calve perthes
4-12 years |
|
|
hall mark of lCP
|
limping pain worsend by activity relieved by rest
goes to knee |
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tx of LCP
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contaiment close observatin bracing orthose and surgically oestotmes
|
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what will be seen on LCP in radiograpy
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wide articualr space the necorsis
|
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SCFE is associated with what
|
obesity deficent gonada develpmentd and hypothrydoidsm
|
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Tx of SCFE
|
pinning external feixation bone grafts and casting
|
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nonpulsatiel swelling of posterior aspect of knee
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pepleit3e cyst baker cyst
|
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tx fo baker cyst
|
Not neccessary
|
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Tx of OSD
|
resloution over 12-24 months on NSAIDS
|
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osteosarcome can be increase by what
|
radioation
|
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tumor in midshaft
|
ewings
|
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where does osteomsacroma go
|
lung
|
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herinamation of bowl withoust a sac
|
gastroschisis
|
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SCFE tx
|
pinning external fixation bond grafts and casting
|
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Radiograph of SCFE
|
medial displacement of epiplysis ice cream off cone and wide growth plaste
|
|
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inferitliy ddf
|
cystic fibrosis
klinefielter kataergenters |
|
|
what infection are increase in cF
|
psuedomenas
saueru retropheral abcess bacterial trachie H influenz epiglottis |
|
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dx of epigolits
|
laryngoscopy visulationa
get ready for endotrachea intubaiton and tarachesotyomy |
|
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contra to breat feedin
|
TSH GV
Toxo syphillis HIV Galcocestima Varicllea |
|
|
Epilgolits presents as what
|
hyperextedn neck and tripod postion
|
|
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barkying couph
|
croup
|
|
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tx of croup
|
epinephrine and cortiocsteroids
|
|
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PDA open and close
|
Close with indomethacin
open with prostagladine |
|
|
Forgien body in baby
dx and tx |
ball valve mechanism
bisulatizon with rigd bronchoscope |
|
|
PKU is a defect in what
|
phenylainae to tyrosine
increase in phenyalaine phyenylaiane hydroxlase |
|
|
MR plus marfan
|
homcystinuria
|
|
|
different stages of pertussi
|
stage 1 rhinorhea conjcuntival injection aand coug
stage 2 soughing spasm inspiratory whoop facial petechia stae 3 convalescesnt stage |
|
|
dx of gold standard
|
B pertussi
look for incoplemet immunizations and lympocytosis |
|
|
mcc of complication of meales
|
otitis media
|
|
|
mcc of OM
|
strept pneumon
hae influena moraxella catarrhalis |
|
|
mcc complicaton of om
|
mastoiditis
|
|
|
how to confirm chonala atresia
|
inabilit to pass cathere throug nostirl cyanososis relieved by crying
|
|
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mcc of epistaxis
|
picking the nose
|
|
|
ivig
|
itp
gulian barre and kawaski burton and cVD |
|
|
itp tx
|
excellent prognosis with out treamten
recover in 8 weeks use IVIG rapid rise only in <30 platele and contersteriods |
|
|
itp and megakaryocytes
|
noram or increase
|
|
|
aorta radiates to what
|
right sternal border
|
|
|
what not to use in WPW
|
digoxin and Ca blockers
|
|
|
hydorcardons what is contraindicated
|
Castir lavages
|
|
|
apathy lethary anermia clumsines anuse and vmoitntg
|
lead exposure
|
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dx of lead
|
increase of free erytjocyte protporphyrin increase lead excretion
|
|
|
dx of CO
|
carboyxhemoglobi level
urinlaysis for myoglobin obtained |
|
|
tx of vwd
|
tx FFP cryopretpati and
dempression |
|
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when does burton show up
|
6 months
|
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what is problem with burtons
|
tyrosin kinase in b cells
|
|
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what is the problem in chroic gran dx
|
defect in NAPDH oxidase
|
|
|
infection of what in cGD
|
increase in catale postive organims
|
|
|
Rubella in neonates
|
cataract deafness micorcehaply
igur Dx IGM |
|
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measles
|
rubeloa
|
|
|
PKU inherintacne
|
autosamal recessive
|
|
|
PKU crazy signs
|
Musty odor projectic vomiting
|
|
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cocaine in neonates
|
samll head growth and cerbral infaractins
|
|
|
ethylene glyco posiong
|
fompizole
comptive antangois of alchol dehydrogenase inhibing metabolism of ethyle glycol |
|
|
neurbolastoma what association
|
nmyc asssociatn
|
|
|
valporic acid in neonate
|
spina bifida facial ab and delay
|
|
|
phenyton in neonate
|
nail hypoplasi bow lip
|
|
|
what does WAGR stand for
|
WAGR
wilm anirdia geniatarlo abnomblarit Rnal problems |
|
|
teratcycline
and doxylicine watch out for lymes dx tx |
enamel hypoplasia
teeth probelms |
|
|
sulfonamide in neonate
|
displaces bilirubin from albuimin
|
|
|
pheonbarbiatl
|
Vit K deficiency
|
|
|
mag sulate
|
respiratoy depression
|
|
|
child abuse
|
fade into the surroundin skin and have differenc colors
|
|
|
small papules or pustules of erymeatou bases
full of eosinophils |
erythema toxicuma
SSSS full of neutrophils |
|
|
milia
|
epstine pearls
that are in the top of the mouth |
|
|
organophosphates
|
Increase ACH
dx decrase in choinerase tx ATROpine and praldixon for nicotino symptosn |
|
|
iron poinsion is going to have
|
collapwse shock and metabolic acidosis
dx iron of >500 tx syrup of ipea antidote deferoxaimen |
|
|
clavicular fracture
|
tx on t indicated
|
|
|
cephalhematome
|
subperosteal bleed does not cross sutre line
|
|
|
hydrocele is collection fo fluid in
|
Tunica vaginialis resolves in most cases by 1 year of age
|
|
|
what is associate with Idm
|
hypocalcemia hypomagnesmisa block surfactan production prone to repsiatroy distress syndrome
Hyperpertrophic cardimyopathe hyperbilirubinea and polcythemia |
|
|
neonatal spesis mcc organism
|
GEL
ampicillin and gentamycin |
|
|
when do you give prophylasxi of GBS in ob
|
<37 weeks
rupture membranes >18 hrs unkneow GBS status |
|
|
maculpapaular raash snuffle hapt sple periostis of long bones thrombycopeina
|
syphilis
|
|
|
saber shin hutchinson teeth rahges saddle noss
|
syphilis
|
|
|
increase of hirspurgs
|
downs
|
|
|
couging or choking with feeds
|
TE fistula
associated with polyhdraminos |
|
|
arthrirs many small joints hands
|
poly articular
|
|
|
what kind of crazy labs in Rheumatoid
|
ESR c reatci proten leukocytosis and thrombycytosis
|
|
|
neonatla lupus
|
rah thromocytopenia and congeintal heart block
|
|
|
brigh red macualr lesion first year of life
|
do not touch them
|
|
|
rash trunck to head
|
rosealo and varicella
|
|
|
major criieria of rheumatic fever
|
aCCES
artitis carditsi chorea erymea subcutatones noduels |
|
|
swollen painful joints and heart murumur
|
rhumatci fever
|
|
|
which one does not lead to rheumatic fever
|
skin infections with GABHS impetigio sterp pyogesn
|
|
|
tx of Rhemuatic
|
penicllin prophylaxis
|
|
|
osler nodes
|
tender nodules on the finger and toe pads
|
|
|
janeway lesion
|
painless hemorrghagei lesion on palms and soles
|
|
|
splinter homrrhage
|
linear lesion beneth the nails
|
|
|
gi prodecures
|
ampicllin
|
|
|
facila neuv in trigemina area of face
introacraina calcifcatin hemiparesia contralater to facela lesion |
Stuge weber
risk for glaucoma |
|
|
partenarl imprinting
maternal imprinting |
prader willi
angelman very happy puppet babies |
|
|
tx and dx for enureiss
|
HP uine anaylysis
reasurasan imipramine adn desmopressin abnormal after 5 years |
|
|
differencie of asperger adn autism
|
more communicateiv appera more socially aware
|
|
|
meinigitis in neonate
>3months |
GEL
N meningitis Spneumonia and Hinfluena n meni college or day care |
|
|
csf shunt infections
|
staphy epi
|
|
|
whooping cough
conjuctival heomrrhage facial petechia < 5 years |
pertussis
|
|
|
Dx of pertussi
|
leukocytosis and lypm high
cultuer of b persutsis supportive care |
|
|
x linked that affects males
thyrombocyotpenia =Peteical rash!!! infections in early infacy otits media an pnemoina eczema may have all the megalys IgA and igE up Igm low bone marrow transplant |
wiskott aldrich syndrome
|
|
|
walk with one and one or more words plays ball
|
12 month
|
|
|
stranger anxiety
|
7 months
|
|
|
pincer grasp
|
9 months
|
|
|
crawl
|
9 months
|
|
|
separation anxeity
stranger anxiety |
12-15
6-9 |
|
|
plays ball
|
12 months
|
|
|
3 cubes
|
15 months
|
|
|
HTN in kids
|
think renal
|
|
|
PDA
|
rubella and premature infants
wide pulse pressue and bonding arteria pulese machinery toand from murmur promine pumonary arter markings tx with indomethancin |
|
|
R to L
|
Ts tetralogy of fallot transpositon tricuspid atreia
|
|
|
Dental procedure prophalyais for endocarditis
urinary of gI |
amoxicillin allergic clindaymycin
ampicllin and gentamicin allergic vancomycin and gentamicin |
|
|
Hep B
|
get at birth
antigen psotive mother requires immune globulin with first dose of vaccine |
|
|
MMR is to be giving when
|
at first year can cauase all the problems of seizuers
along with varicella |
|
|
cystic fibrosis deficieny is what vitamins
|
lost of vit adek
k is loss of II VII IX X |
|
|
not in immunocoimpromised
|
mmr varicella orol polio
|
|
|
egg
|
mmr influenza
|
|
|
Preten immunization
|
immunize at chronologic age
|
|
|
tx of neonatla sepsis
|
ampicillin and gentamycin
|
|
|
RDS
|
first 3 days of life
tachypena nasal flaring retarcit cyansos and grunting |
|
|
which bilirubin is neurotoxic
|
uncongjucated
|
|
|
when does physicologic come
|
after first day uncojuated resloves by 1 week
|
|
|
breat milk jaundice
|
at 1 week of age
|
|
|
what is always present in Truncus arteriouss
|
VSD is alawya present
|
|
|
Transpositon is increased in what type of pt
|
Diabetic mothers and boys
|
|
|
what is the ches radio graph of trasnpsoti of great vessels
|
egg on a string
|
|
|
left lower mid steranl border
never diastolic never greater grade 2/6 |
innocent murmurs
|
|
|
when do you have innocent murmure
|
3- 7 years
|
|
|
how do VSD cuase eisenmenger
|
high pumonar bllod flow increase in resistace
right to left |
|
|
half ot tubers are going to have what on heart
|
rhabdomyomas
|
|
|
DX of tubers
|
head Ct or mri and echo for rhabdo
|
|
|
port wine stain of Strgue weber
|
is upper face an eyelids
|
|
|
respiratory thing in CF
|
nasal polys
|
|
|
interstial pattern in lower lobes
|
mycoplam pneomia mCC 5-15
|
|
|
chlamydia will have what on white count
|
eosinophilia
|
|
|
how to diagnsosi mycoplasm
|
cold hemagglutinis
|
|
|
tx of chyamdia pneumonia
|
ertoymycin and sick contact
|
|
|
M penmoina tx
|
erytromcin axithromycin and clarthmycin
|
|
|
painful ulcers on tongue adn oral mucoas and maculapapular ras on dista limbs and buttocks
|
hand foot mouth dz
|
|
|
herion withdrawal is when
methadone is when |
48 hours
2-6 weeks |
|
|
herion vs gluocse withdrawla
|
IDM have ruddy pelthor complex not much dirrhea fever high pitched crying sneezing vomiting poor feeding
|
|
|
what is the mcc JRA
|
pauciarticular
|
|
|
what are the labs for pauciarticualr
|
ANA+ RF-
|
|
|
what are the skin manifestinton of kawasaki
|
mucous membrean strberry touge and edame of hands and feet dequamation fo finger tips
|
|
|
recurrent epidsode of angio edema provoked by stress or truama
|
C1 esterase deificiey hereiditar nagioedema
|
|
|
hwo to diagnsos herediar angioedema
|
totoal heolytic complemtn CH50
|
|
|
recurrent menigocooclal or gonococcal infectoino
|
terminal complement deficiency inabilty to form MAC
|
|
|
oculocutanes albinishm neuropathy and neutropenia
increae in s pyogenes s aures and pseudomoas |
chedaik higashi
|
|
|
what is the defect in ch syndromw
|
AR defect in neurtophil chemotaxis
|
|
|
oral polio varicella and mmr should not be used in
|
immunocompromed and pregnag patient except for HIV
|
|
|
when do you hospitazile RSV patients
|
92% <34 weeks age <3 months
|
|
|
age in epiglottis
|
3-7 years
|
|
|
postion in epiglogtittis
|
snifing dog postion
|
|
|
what do you do first in epiglottis
|
secure airway before diagnosis
|
|
|
trachetis is by what organsism
|
s aureus
|
|
|
Retro is when and pertonisillar is when
|
6 months to six year
>10 years |
|
|
which meningits will give you petechial rash
|
ne meningitidis
|
|
|
do before lp
|
ct scan
|
|
|
what is pertussis
|
G- bacillus<
|
|
|
when do you hospitalzie pertussis
|
<6 months of age
|
|
|
what does fith dz worsen with
|
fever and sun exposure
|
|
|
where does fith dz start
|
arms
|
|
|
what happens in fift dz in congential
|
hetal hydrops and death
|
|
|
rare complication of measles
|
subacute sclerosin panencephaltits
|
|
|
what can happen with complication of measles
|
febrile seizuers
|
|
|
oral ucles with rash
|
hfmouth dz cox a
|
|
|
conjugated ddx
|
extrhepati cholestats biliary atresia choledocha cyst intrahpatic cholestatiss
|
|
|
Unconjuaged
|
Physiologic jaundice heomlysis breast milk jaundice
|
|
|
stool and urine in jaundice
|
light colored stools adn dark urine
|
|
|
air in GI tract
|
TE fistula
|
|
|
reatined amnitic fluid promine perihilar streaking in interlobular fissuer
|
Trasinet tachpnea of new born
|
|
|
carse irrgeular infilitrate hyperexpansion and pneumothoraces
|
mecomium aspiration
|
|
|
nonspecific patchy infiltrate sneutorpeia trache aspirate adn gram stain
|
congential pneumoia
|
|
|
how to mointor mothers for surfanctan
|
lectihin sphingomyelin ration and phosphatidlyercol
|
|
|
spasti pareis of any or all limbs
|
Pyramidal mMR
|
|
|
low grade fever fro severl days before seizuer oneste
|
complex febirle seizure
|
|
|
what to aviod in febirle seizure
|
asprin
|
|
|
what is seen in afro kids
|
AML
|
|
|
tx of luekmia what to watch out for
|
tumor lysis syndrome
hyperkalemai and hyperuricemia |
|
|
sacrom of neuroectoderma orgin
|
ewing sarcoma
|
|
|
arsisn from osteoblast of meschyam origin
|
osterosarcoma
|
|
|
what is elevated and poor prognositic factor
|
alkaline phospatas
osterosarcoma |
|
|
scid need what prophylaxis
|
PCP
|
|
|
bleeding ecema and recurrent otitis media
|
Wiskott aldrich syndrome
increas in atopid disorder lympma leukema and spneumoia |
|
|
what do you treat CGD with
|
daily tmpsmx
|
|
|
ataxia telang is a defect in what
|
DNA repair defect
|
|
|
pimmunoglubli level drops in 20 and 30
|
common variable immunodeficiey B and T cell problem
|
|
|
burton has increase in what organism
|
encapsulated
|
|
|
tx of b cell problems
|
IVIG except for IgA
|
|
|
what fungus is increase risk of with CGD
|
aspergillus
|
|
|
study of choic for malrotation
|
upeer Gi
|
|
|
mcc cuase of bowel bostrucitn in frist tow yearl of life
|
intussusception
|
|
|
abdom pain vomitin and blood per rectuem
|
intussection
|
|
|
mother with pku need to restrict diet when
|
before conception
|
|
|
tx pku
|
decrease phyenalanin and increase tyrosine
|
|
|
walks up down steps six cubes
tow word pahrase follwo tow step commands |
2
|
|
|
penemonia in 0-28 dyas
|
GEL
tx with ampicllin plus gentacimin do full septic workup including lubmar puncture |
|
|
pneumonia in 2 motn to 5 years
bacteria |
s punemonia h influeze and staphylocuccus
use cefuroxime or ceftriaxone |
|
|
pnemonia with interstital pattern
|
mycoplasma
|
|
|
pneumina with hyperinflation or groung glass apperasce
|
chymaydia
|
|
|
varricella is live or dead
|
live
|
|
|
chroni regional lypmpadentits fever cat expures
|
warthin starry stain
|
|
|
tx of cat scrach dx
|
resloves spontaeou 2-4 months
|
|
|
ataxia masklike faces drooling tics and irregular eye movements
|
ataxia telangeictasia
|
|
|
do NSAID help in OSD
|
No
|
|
|
tx of Legg calve perthes
|
containment
self healing process |
|
|
what is abnormal in lead where does it go in the body
|
metaphyes of long bones
>10ug/dl |
|
|
what is given babies to stop nesiseer gongrrohes give to babies
|
silver nitrat drops or erthoymcyin drops
|
|
|
tx of chlamydia conjcitivis
|
topical and systemic antibiots ertyhromyucin chalmydia pneumonia
|
|
|
chemical
gono chymila |
24
2-5 5-13 dayas |
|
|
gonochonal conjuctivits
|
ceftriaxon
|
|
|
IgA have recurrent what
|
gastroinstinal infection
|
|
|
pt with absent lymph and thymus
|
SCID ada deficiency
|
|
|
lead posion in kids
|
succimer
dimercaprol in adults |
|
|
tx of OM
|
amoxicllin
|
|
|
tx of stype
|
tx woarm comress and topica antibiotics
|
|
|
chalaxion retention of secriton of mebomain glands
|
require excision
|
|
|
chlamdyida conjucdtivit
|
5-23 days
|
|
|
corneal abrosion
|
pain photophiba tearing and decrease vision
dx with observing the ever under lue filter lighe after instillatin of fluorsecien tx topical antibioties |
|
|
arm adducti and pronated internaly roated
|
erb ducenn
|
|
|
reticular granular patter in preterm
|
hyaline memebrane or respiratoy distress syndrome
tx with surfancty |
|
|
12 year old fever sore thoart
follicualr conjuctivit |
adenoviurs
tx supportive |
|
|
HIV in neonates is reduced by
|
C section prenatal intrapuart and neonatla ZDV
|
|
|
most common complciaton of mumps
|
menigoechphalmyeltisi
|
|
|
noctural pruuin in kids
|
enterbiasis tape test
tx is albendazole mebendalo |
|
|
salmonelala
|
eggs milk and poultry
|
|
|
shgiela and campybacter
|
person to person spread
|
|
|
yersinea
|
tramitted by pets
|
|
|
12 hours and food
|
staph aures
|
|
|
acute blood diarrhea in colon
|
e histolytica
|
|
|
giardia
|
cyst ingest from food
|
|
|
c diffcle
entamoeba giardia |
tx with metronidaoznle
|
|
|
loud s1 and fix s2
diastole murmure |
endocardial cushion defect
|
|
|
treatment of coarction
|
prostaglidnins
|
|
|
loud harsh systolci murmur and single s2
|
TOF
|
|
|
what are happening to lungs in tof
|
lung feilds clears
|
|
|
complication of TOF
|
crebral thrombosi bc of polycytmea nd dyhdration
|
|
|
decreae pumonar blood flow
s2 single left axis deviaton and left vertircular hypertopy |
Tricuspid atresia
|
|
|
how ot confirm myocarditis
|
endomyocardia biopys confirm the diaoas of
|
|
|
when do you see fungal infections in endocartditon
|
heart failure
|
|
|
milia are where
|
hard palates
|
|
|
what is seen in sturge weber in Ct
|
calficitaon
|
|
|
erb can have what
|
respiratory paraalysi c 435
|
|
|
macroglossi
|
down
bicktwitth wideman |
|
|
pulmonary hypertesion in newborn
|
give 02
|
|
|
most common age for pertussis
|
<5 years
|
|
|
what are the labs for pertussis
|
leukocytosis by lymphocytoiss
|
|
|
what is the metablit that acetamionphen makes
|
NAPQI that is hepatotoxicty
|
|
|
baby with musty order
|
branched chain alpha dehydornes deficieny
maple sure urin dz |
|
|
apperance pulse
grimace activity respiration |
pink
>100 cough active good |
|
|
tx for lymes
|
<8 amovicillin
> doxycycline alternate cefuroxime |
|
|
sudden cessation f motor activity or speed
|
absense
|
|
|
what is absenc provoked by
|
hyperventilation
|
|
|
most common worm infect in GI
|
enterbius
tx with mebedazole all members should be tx |
|
|
roll prone to supine
|
4 months
|
|
|
TE fistural
|
fistula between the trachea and the distal esophagus
allow ari itno the stomach and small intestine |
|
|
pathogen associated with galactosemia
|
ecoli
|
|
|
copy a trignal
|
5 years
|
|
|
willima syngdormw
|
ad
deltion on chromso 7 reomves r make the elastin gen nofuncitonal FISH elf like |
|
|
willimas deletion in what
|
chrom 7
|
|
|
anaphylacti rx
|
1st step is ephinephrine
|
|
|
sondboes fever hepatmagl wheezin pulmar dx
eosinphil |
viscer larv migrans
|
|
|
5-7 dyas after uri
|
reye ammonia tranmsin hypoglycems
|
|
|
liver bipys of reye
|
noninflammatory fatty infiltration
mitocondriad get fucked up |
|
|
meningitsi in sickle
|
strep pnumoenia
|
|
|
lescho nyhan
|
HRPT purine
excess urin acid HPRT enzyem |
|
|
vomiting hyperpnea fever lethargy meatn confusiong
|
Aspirin mild
|
|
|
how does aspirin cuase metabolic acidosis
|
krebs cycle inbigited
|
|
|
diagnois of arboviruse
|
Img elisa
|
|
|
nessierem menigitsi how to diagnsosis without lp
|
culture the purupsa
|
|
|
chymdial
|
hyperinfalation and ground glass
no fever |
|
|
mycoplasma
|
interstila
|
|
|
pnumatolece in xray
|
staph aures
|
|
|
becarful osgood schlater dx is the same age as slipped capital
|
dz self limiting resolve is 12-24 months
|
|
|
cluttn joingts
|
symmeter painless swelling of knes
|
|
|
scabies diff kids
|
no burrows
|
|
|
hutchingson teet
|
peg shaped ntoche nectral incios
|
|
|
rahges
|
peroir fissure or crackes in skin
|
|
|
subaleal hematoma
|
leave it alone
|
|
|
low DHT high testo
|
5 alpha reductase
micropens and hyospadia with urine meat locate on perimue undesced inguinal cancl |
|
|
fever low grade or absent sart on cheek conflute
maculpapular rash trunk facial rahs lacy reticular apperance pruitic desqumatn |
erthem infectisoum
|
|
|
adeonpathy low gread fever arthrlaig coryz and conjunctivit
|
face or neck spreading in hour to trunk and extermtis
|
|
|
hypopsoptema deefect in thproximal ren tublar reabsopr of phsot hae cuas by
|
failer of 25- to 1- 25
familiar ox xilingk hypophospatemia bwoing of leg waddling gait |
|
|
nitrate interacts with the hemoglobin or RBC
|
blood samples appera chocolat brown do not turn pink when expose to air
|
|
|
methemoglobienma
|
get a methemogloibn leel
antidote is methlene blue |
|
|
childoho histocytosis
|
hand schuller christan dz
|
|
|
blood pku leves
|
kept below 6
|
|
|
streptococcus agalctia
|
group b
|
|
|
Hb H
|
4 beta chains bc alpha chains are not coming together
|
|
|
low IgA and Ige skin loses elasticiyt infection atxias telangestas
|
ataxia telangectast
|
|
|
freideric atxas
|
atxiad dysarthic speed cystagum skeltat abnormalti
|
|
|
ewings presents at what year
|
teenage years
|
|
|
diffuse mottled lytic lesion medularry cavit and cortical hone
|
ewings
|
|
|
dislocation of lens
|
marafans fibirlin 1 gene
|
|
|
homocystinur
|
cystathion syntats deficien methionie
fari comlexion thrombemolc event osteopro lens dislocation downward |
|
|
mytonic muscular dystrophy
|
autosmoal domint disea
2nd progress muscle wasting distal muscle ofh hands posterior forearm muscles anterior compart of lthe lowere legs temporal wasting thin cheeks upper lie in V testicular atroph fronat bladness jhypthryoidsm |
|
|
NEC
|
tx bowel rest
amp and gen preterms that dont breath well air in bowel |
|
|
retinoblastom
|
bilater brian and liver mets
only one eye |
|
|
congetial catarcts
|
both eyees
|
|
|
overlapping fingers small chin vsd
|
edwards
|
|
|
willians syndrom2
|
supravalvular aortic stensosi
|
|
|
gyncomatstia in 14 years
|
ulitat later
from prebuetr reassuarnce |
|
|
gullian barrie
als |
motor and sensory
motor |
|
|
gullian barre
|
tx plasmaphereis
ivig csf protein elevate |
|
|
septic arthis of hip
|
stahpy aures
do surgery bc can lead to AVH 100,000 |
|
|
HUS can lead to what problem
|
renal faliure
|
|
|
subaranoic heommarge
|
AVM history of siezures
|
|
|
homocystinurea
|
mehtionie meatbolims erros 2nd ot cystation synthase deficeiyt
thromboembolic events homocytinureai lens downward |
|
|
to of homocytinuera
|
B6
|
|
|
krabbe dz
|
defeiceiy in beta galctosideas
no myelin mR blinde deafness parlaysis perphera motor sensory neropath and seaizure no hyerpcoagel state |
|
|
tay scahe
|
heta hexsaminda A derficney mR blinde chrer remaucl weaknes and sezuers no hypercuagle state
|
|
|
cyclical vomiting
|
mom has headache
|
|
|
iron
|
vendodelation and increase capilarr permabilt and hypotensison
then lactic and citric acid liver necrosis coagulapthy drownisnes ssiezuer coma Iron serum iron level tx leac syrup sytor no activate charcaol |
|
|
uri and then hip hursnt
|
traseint syovitos of the hipe
consist of inflammation and swellin of the tissues around the hipe joitn bed rest and |
|
|
asprin in kids
|
kwaski dz and JRA
|
|
|
give food at
|
6 months
egg whites at year |
|
|
systemic JRA
|
hgih grade feve rmaculpapular rashe hepatspleomgeal ymphadeopath pleorperciardio
Rf is rarly psotion NSAIDS myocardit or anterior uviets |
|
|
SID
|
peaks at 2-3 motnhs
most common up to one year |
|
|
friderci ataxia mcc cuase of death
|
cardimyopahty and respirato complciaton develpin up to90% degenartoof the spianl tract
diabetes skelta defomrit has HCM |
|
|
water hous redercdis syndromwq
|
suddern vasmot collapse skin rash
adreanl heomrrages vasomto collaps large petchia purpuri lesion |
|
|
siclek cells anemai
|
hemolytic anemia
|
|
|
why no clinical feature in Sickle cell
|
still HbF not muc HbS
|
|
|
Sicke cell from 2-4 months
|
hemolytic anemia developa
|
|
|
5-6 months
|
hand foot syndrome dactylites painful smmetri sweellin fo the hands and feet secondary to poor blodd flow to the expandi marrow spaces
|
|
|
ssara
|
778-2649
|
|
|
all is more in what
|
white childer increase in down atxia telagectase von reckliand
|
|
|
least favor for all
|
yougher than 2 years great than1000
beign black |
|
|
hyperkalemai hyperphosphatema tetany calcium phsophat in renal tubles
|
tumore lysis syndrome
|
|
|
short stature bitermpoar visula field defect
calcification at the sella turcia |
craniopharngioma
supratentoraila |
|
|
decreaes visular acuity proptos and asymmetri cystages
|
opticl gliomase
|
|
|
first step in htn or renal problesm
|
urinalysis
|
|
|
krabbe
|
myelin destrcution
AR deficity in galctocerbroside |
|
|
orbital cellulits
|
pain with eye movements
|
|
|
csf glucose
protein cells |
50-100
20-40 |
|
|
Gram neg rods
|
listeria bacillus
pseudomaas heaomphil klebisel legonella |
|
|
recurrent sinoplumoary and diarrhea
|
cF CF CF
|
|
|
severly neutropenic patiens
|
staphyolocouu psudomas and aspergillus
|
|
|
medulloblastoma
|
vermis
mstatsta throug the CSF |
|
|
astrocymoa
|
cerberlla hemishpeere
which is going to be arms |
|
|
eosionphils
in breast feed women |
think allergies
vomiting and bloddy diearea milk intolerace of newborm give soy proten |
|
|
CFTR is a what
|
deletion on 7
|
|
|
parinaud syndromw
|
paralysis of vertical gaze that may be associate with pupillar distrubace and eyelid reatioran
rostra mideran at the level of superio collicu and cn endocrine problems |
|
|
hypertion menatur ab pain and vmoint lung metstaes
|
wilmes
|
|
|
minimal change dx tx
|
steroids
|
|
|
hangerhans ishtocyosis
|
lytic hyerpcalcin in patient
|
|
|
cerberal anoxi
|
mcc of cerebarla palsy
|
|
|
sickete trait
|
is 40% and get painless hematureia
recurrent in preganct women |
|
|
pseudomaonsa
|
cefepimen imipenm/cilastation
ceftazidiem ticarcliin plus amikacin or gentamycin |
|
|
fanconi
|
pancytopenaia congential anomaleis hyperpigmentatio on the trunk neck and intergion area cafe auliat spot shor stater upper limb abnomarl hypagada skeltanomalek
renal malfomations |
|
|
diamonad blackfa anema
|
pure red cell aplsa
palor and porr feeding |
|
|
what will be the bone marrow in aplastic anemai
|
hypoceulluarl and decrease in all cell lines
and fayy infilatration of marrow |
|
|
norm normic in pretem
|
anemaia of pretem
|
|
|
bedweeting
|
depression
imipraine |
|
|
beckwith wiedmann
|
macrosmia macroglossia omphalocel hypglcema and hyperinsuliema
promeitn eyes proimet occiupt ear |
|
|
BW mechain
|
chromsome 11p encoding for IGF-2 macrosmia hyplgycemain sever intracta subto pacreatmoy
|
|
|
hemiplagia after seizure
|
todds paralysis everything elese is normal
|
|
|
use cefotazixme or cerftraion
|
menigits post 3 years old
|
|
|
hydrourez
|
increase hemgolbuin F use in
in acute pianful episode more tha six episode in one year increase Hb F by stimulation ertyojmp osis |
|
|
lung infation in sickle cell
|
actue shnydomre
|
|
|
nasal polyps
|
cystic fibrosis
|
|
|
fancio
|
low RB
low platelet low WBC limb and renal and dark |
|
|
tuner is Y
|
increase risk of gonadablast
and they are going to need to take it out |
|
|
autosoma dominat collage deficiey
hypermobile ears and velvey skin hyperextersbile poor wound healing hyperextesibel dilcoatsmitral valve prolapse |
ehler danols syndromee
|
|
|
tall stature long libms scolios pedctus excavatums
|
lens sublzxiton myopia retianl detachemnt
|
|
|
compian of orbital pian decrease vision protosis conjuctival edeam and eylid swellin and fever
|
orbital cellultisis
|
|
|
tx of orbirat celluutis
|
anti biotis and drainage
|
|
|
uri hypoglycemia menta stat change sseizuers apneica
|
reye syndrome
|
|
|
tx of CAH
|
hydrocortisone
sodium repalce increase doese of hydrocortiosne |
|
|
what is high and low in CAH
|
17oh progestorne rinin and psotassium
soduimcholerema aldosterone |
|
|
large toughe umbicla herina and large fontanel muscle ont is decrease constipate
|
hypothrodism
|
|
|
mcc of hypothyrosidms
|
thyroid dysgensis
|
|
|
falccid paralysis of lower extremeti absent deep tendonrelfex club ffot subluxed hips hydrocephal
|
myleomengocele AFP and acetychonesteasr
|
|
|
what is the first thing to go in gullian barre
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tnedo relfex are lst early weaknes progess to motor and sesory nerves
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what is seen in muscle biopy of duchenne
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necrosis fat cell and fibrous tissue
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mcc of death 1-12
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sudden infant
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what does goat milk drinking babies need
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folate
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when are foods introduced
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4-6 monts
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line in kids
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use interocuous
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doll like face with fate cheek thin extermites and progtuberan abdomen
low blood lactic acidosis 3-4 motnh ol |
glucose 6 phoast defeice
type 1 glycomen von gierkes Ex def g-6 phostase defeciney |
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floopy baby with feed diffuiclty macroglossia and heart failure matt got it on one of his tests
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maltase deficeiy
floppy baby |
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glycone storage !!fasting ketosis and normal blood lactat and uric acid concentratoin
spleonmegaly normal indy |
deficeiny of glycong debraching eznym activity
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progressive cirrhosis of liver
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dfeicney of branchin ezyme activity
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alkaia
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is need to go in and check with scope dont add anything
bc they may need to |
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infaitl spam
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associated with tubler scelrosis
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1st in diaphermatic herina
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decompress bowel with orrogastric tube
immediate plsacet contious scutin preve bowel distenison |
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cut of for unbical hernia
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1 year of ages
or exceed 2 cms |
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prematurea pubis
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cns 50% require ethroug evalutioans
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molibirum rash
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kawasakis
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mcc for conjugated bilirubine
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biliary atresia
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gilbert and carnarj
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both unconjugated
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subarachond hemoorage dilation of the entrie ventricular systemenlagemtn of subarachonio space
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IVH
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HSP
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igA vasuclitis and
then ofn the folliucrease |
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cervial lymphadenopath protruding abdomne chrerry rep spot hypotonia heaptospleonmegaly
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niemassn pick
sphingomyelin reticluendotheial cell of live spleen bone marrow and brain |
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hyperacusis metnal reatardi seizure chrer rem amacualr no cerival lyphgdepathy
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tay sahcs
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asthma
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dont give oral presidoen
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actue chest
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inflitation on xray
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measles
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leukopenaia and thrombocytopeian
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club foot
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turin in and addbictuon of the forefoot
serical streching and casting serial plaster cast |
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unresponive and blue single s2
and vsd |
cyanto spells acute with eating
TOF |
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neurofibormatots
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hamartomas of the eye
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flucatn cervial lyph nodes
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staphy idicloxalciln cover strep a and staph
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widep pulse pressure and bounding arterial pulses
2 nd left intercosta spance machiner or to and form murmure promeint pumoary artery and increaed pumomary vascular marking |
PDA
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complication of PDA
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infecti endocatiron and CHF
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CHF metabolic acidos and lower body hypperfusion uper or lowe extermitn puls delay
hypertension in the right upper exterem versus the left around the lfeft subclavien |
coarction
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lef sternal border at hte thid to fouth interconsta spacerig notchin from enlargment of intercoas providn collater blood flow
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coarction
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cyanosis delayd grow and dveloement dyspnea very soft becuase of the pumoary stenosis s2is single and soft
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TOF
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what is required for VSD
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antibiot prophylasi for endocardits
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enlarde right atrium and ventricle
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ASD
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