Pediatric Boards Xv.) Blood And Neoplastic Disorders

Front 1

What is the most common primary renal tumor and second most common abdominal malignancy in childhood and describe it?

Back 1

Wilms Tumor or nephroblastoma is a kidney tumor made up of embryonic tissue, usually unilateral and bilateral 5%

Front 2

What are signs and symptoms of Wilms tumor?

Back 2

a large, firm, palpable abdominal mass that does not stretch across the midline, hypertension, malaise, fever, hematuria, weight loss

Front 3

What is WAGR?

Back 3

Wilm's tumor, aniridia, genitourinary anomalies and mental retardation, d/t deletion of 11p13

Front 4

What is the treatment for Wilm's tumor?

Back 4

Chemo, radiation, and nephrectomy...all depending on staging

Front 5

What is the histology of a Wilm's tumor?

Back 5

Embryonal renal neoplasm where blastemic, stromal and epithelial cells are present; a tumor of the developing kidney

Front 6

What age is Wilm's tumor usually diagnosed?

Back 6

Usually at less than 5 years of age; usually at 2-3 years

Front 7

What is the most common presentation of Wilm's tumor?

Back 7

less than one year of age with abdominal pain/enlargement or mass with microscopic hematuria

Front 8

What is the most common extracranial tumor of childhood and most frequent of infancy?

Back 8

neuroblastoma

Front 9

What tumor presents w/abdominal masses arising in adrenal glands or paraspinal sympathetic ganglion?

Back 9

neuroblastoma