Lisa Nephro 1 - Ucla - 13

Front 1

what's most common and best prognosis of HUS? and cause

Back 1

D + HUS: E.coli

Front 2

anemia, hemolysis, leukocytosis (30-40K) thrombocytopenia
-irritable, CNS dysfxn; pale, fussy, sz; coma;
-what GI sx?

Back 2

HUS;
-/+ diarrhea: bloody, mucoid; colonic involvement (leukodcytosis); rectal prolapse, bowel necrosis

Front 3

HUS tx?

Back 3

dialysis for renal failure; No anbtx (worsens)
-transfuse for hct < 20;
-supportive care

Front 4

?prevent HUS?

Back 4

cook meat well; handwash; isolated infected pts

Front 5

what makes good prognosis and poor prognosis of HUS?

Back 5

D + ; good prognosis
- Poor prognosis: prolonged anuria (> 7 day)
-renal scarring on bx; and severe CNS involvement

Front 6

3 yo fussy, pale, puffy; wBC 25/5/15/ plt 80; bmp: K 6.1, HCO 11; bun/cr: 40/3;
-dx? and tests?

Back 6

HUS;
stool for E.coli;
-send coombs, (+ in pneumoccocal HUS)
-send C3, C4 - low in genetic causes of HUS)

Front 7

defenine HTN in kids: what do you always check for ?

Back 7

> 95th % for age and height
95% for SBP = (age x 3) + 100
95% for DBP (age x 1.5 ) + 70
-3 separate measurements;
Pre htn > 90%

Front 8

most common cz of htn in kids?

Back 8

renal causes, but also check for coarc;
1) parenchymal (Acute GN, scarring: UTI) vs
2) renovascular - narrowing of renal artery (renal artery stenosis, UAC, NF1 ~ cafe au lait - Neurfibromas pressing on renal artery)

Front 9

infancy, HTN, what's most common form? ambiguous genitalia

Back 9

CAH: 11 and 17: HTN;
most common 21; but doesn't cause HTN

Front 10

goiter, taccy, flushing, HTN

Back 10

hyperthyroidsm

Front 11

striae, moon facies, buffalo hump, h/o steroid exposure

Back 11

cushing's disease- overproduction of cortisol

Front 12

teenage period, HTN:

Back 12

drugs; need tox screen: + amphetamines, cocaine, PCP, cough/cold meds

Front 13

NB most common htn?

Back 13

RA or RV thrombosis
-RAS, Cong renal diz, coarc

Front 14

HTN in 1st year life ?

Back 14

coarc, renovasc diz, renal parenchymal diz

Front 15

infancy-6 yo HTN causes?

Back 15

renal parenchymal diz, renovas diz

Front 16

Renal aretery stenosis, cafe aulait spots, pheochromocytoma ~ ?

Back 16

Neurofibromatosis 1

Front 17

sore throat, coca coala colored urine, HTN; ? Dx, tx?

Back 17

PIAGN, diuretics

Front 18

flugshin, sweating, HTN; dx/tx?

Back 18

pheochromocytoma;
alpha beta blockade

Front 19

recurrent UTI; dx/tx?

Back 19

renal scarring; ACE

Front 20

what condition is ACE I CI?

Back 20

bilateral RAS

Front 21

what is beta blockers and central alpha agonists CI?

Back 21

depression

Front 22

what is beta blockers CI?

Back 22

asthma and diabetes

Front 23

8 yo w/ BP 130/85, scoliosis, cafe au lati spots,
-cause, inheritance? ~

Back 23

NF, AD, ~ pheochromcytoma

Front 24

8 yo w/ bp 150/75; dark cola colored urine; h/o sore throat; cause/tx?

Back 24

PIAGN; diuretics

Front 25

14 yo w/ bp: 140/90?

Back 25

check urine tox;
increased incidience of systemic diz (females)

Front 26

when see > 10 WBC,
- when see no infex?

Back 26

viral UTI, GN

-no infx: TB, appendicitis

Front 27

urgency, frequency, dysuria, no Fevers, or systemic signs: ?

Back 27

acute cystitis - inflamm of bladder mucosa

Front 28

fever, flank pain, Vomiting,

Back 28

infection of kidney: pyelo

Front 29

what imaging do after dx UTI? whats most common complx > UTI?

Back 29

1) upper tract: U/s (hydronephrosis)
-CT or IVP (

2) Lower tract: VCUG
- detects: VUR - most common complx (vesiculorenal reflux)
detects PUV

Front 30

males, proteinuria, hematuria, deafness; ? inheritance

Back 30

Alports;
-x-linked - defect w/ collagen IV; Kidney, eye, ear

Front 31

young kid w/ light hair, skin presents w/ fanconi syndrome (which is what? )

Back 31

cystinosis;
Fanconi syn: RTA, glucosiuria, phosphaturia ( but low serum phos) due to buildup of cystine chrystals --> renal failure/transplant

Front 32

when liver can't break down oxalate

Back 32

hyperoxaliuria, kidneys become 2 hard rocks: need liver and kidney transplant

Front 33

most common renal tumor?

Back 33

wilm's tumor

Front 34

nephrotic syndrome, diffuse mesangial sclerosis, ambig genitalia;
-risk for wilm's and male psueduohermphrodism

Back 34

drash syndrome

Front 35

short, renal rickets: renal osteodystrophy;
HTN, anemia; Late electrolye disturbances

Back 35

chronic kidney disease (CKD)
- (hyperkalemia - indication for dialysis)

Front 36

dysplasia, U/L agenisis; branchial fistulas;
-kidney and ear problems, pits in ear/neck; hear loss

Back 36

branchio-oto-renal syndrome

Front 37

renal failure w/ oligo; small, post set ears, micrognathia, beaked nose, wide set eyes, pulm hypoplasia; small chin;

Back 37

Potter's

Front 38

dilated urinary tract, dysplastic, aplastic kidneys, hydronephrotic kidneys;
- no abd muscle, cyrptorchdoidism

Back 38

prune belly

Front 39

renal aplasia or hypoplasia, double colecting system; u/L aplasia of pec major w/ ipsalateral

Back 39

?

Front 40

renal agniomylipomas, cystic kidneys, renal cell ca.
-adenoma sebaciums, epilepsy, CNS tubers, retinal phakomas

Back 40

Tuberous sclerosis

Front 41

hematuria, protienuria, GN,
-lower limb - palpable purpura, abd pain, arthralgia;
-check for ? or ~ what GI d/o?

Back 41

HSP; need to check for hematuria
-h/o arthralgia in Ext; GI involvement
-intussusc