Icm Fall Final

Front 1

What are the 4 defects in the Tetralogy of Fallot?

Back 1

1. Ventricular Septal Defect
2. Pulmonary Stenosis
3. Overriding aorta
4. Right ventricular hypertrophy

Front 2

What are the clinical manifestations and what do you see in imaging studies with Tetralogy of Fallot?

Back 2

Clinically you see pulmonary stenosis and hypoxic spells.
EKG- Right Axis Deviation and right vent hypertrophy.
Xray - boot shaped heart

Front 3

What are the clinical manifestations and what do you see in imaging studies with transposition of the great vessels?

Back 3

Clinically you see cyanosis.
EKG- Right Axis deviation and right vent hypertrophy
Xrya- cardiac shadow looks like a egg on string (narrow superior mediastinum)

Front 4

Treatment for trasnposition of the great vessels?

Back 4

Prostaglandin E1 to maintain ductal patency.

Front 5

What are the clinical manifestations and what do you see in imaging studies with Tricuspid Atresia?

Back 5

Severely cyanotic clinically.
EKG-left vent hypertrophy
Xray- normal or mildly enlarged cardaic silhouette

Front 6

What are the clinical manifestations and what do you see in imaging studies with Truncus Arteriosus?

Back 6

Systolic murmur heard with possible systolic ejection click.
EKG - combined vent hypertrophy and cardiomegaly
Xray- increased pulmonary blood flow

Front 7

What is Total anomalus pulmonary venous return and clinical manifestations?

Back 7

All of the pulm veins fail to connect to the L atrium and return abnormally via the R side of heart.
Clinically you see hyperactive R vent impulse with widely split S2 and systolic ejection murmur at the L upper sternal border.

Front 8

What are the clinical manifestations and what do you see in imaging studies with Hypoplastic Left Heart syndrome?

Back 8

Clinically:low cardiac output
EKG: R vent hypertrophy
Xray: cardiomegaly
this is the most common cause of death from cardiac defects in the first month of life.

Front 9

Clininical manifestations of VSD?

Back 9

Pansystolic murmur, heard best at the left lower sternal border
usually these close spontaneously

Front 10

Clinical manifestations of ASD?

Back 10

Prominent lR vent impulse at the L lower sternal border that can be palpated.
Soft systolic ejection murmur in the region of the R vent outflow tract and a fixed split S2

Front 11

Clinical manifestations of PDA?

Back 11

widened pulse pressure,
continuous machine like murmur

Front 12

Clnical manifestations of Coarctation of Aorta?

Back 12

femoral pulses are weaker and delayed compared to R radial pulse.
BP in LE is lower than UE
s3 present
there maybe a hx of leg discomfort with exercise, H/A, or epistaxis, HTN maybe present

you might also see rib notching

Front 13

What are the defects of DiGeorge Syndrome?

Back 13

cardiac defects
abnormal facial features
thymic hypoplasia
cleft palate
hypocalcemia

Front 14

What are the manifestations of Digeorge syndrome?

Back 14

hypocalcemic tetany, pyogenic infections, partial or complete T cell deficiency, congenital heart disease, hypoparathyrdoisim, convulsions

Front 15

Clinical manifestations of Down syndrome?

KNOW THIS!

Back 15

Increased risk of leukemia
hypotonia, congenital heart disease, duodenal atresia.

Front 16

Feaures of congenital rubella syndrome

Back 16

intrauterine growth restrition, microcephaly, microphtalmia, cataracts, glaucoma, hepatosplenomegaly, jaundice, PDA, deafness, blueberry muffine rash, anema, leukopenia
rose colored spots on the soft palate called forchheimer spots

Front 17

What do you know about Turner's syndrome

Back 17

childhood obesity, ovarian dysgensis, lymphadema, web neck, XO choromosome,

Front 18

The most common heart defects in Turners syndrome?

Back 18

Coaractation of the aorta.
Bicuspid aortic valve leading to aortic stenosis.

Front 19

Marfan Syndrome?

Back 19

Above average height.
Arachnodactlyl
doliochostenomelia
scoliosis is common
pectus excavatum
pectus carinatum

Front 20

Major cardiac problem in Marfans?

Back 20

dilated aorta or aortic aneurysm.