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12 Cards in this Set
- Front
- Back
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What is the most common tumor of infancy?
- genetic? - predisposing demographics? - two phases of evolution? - three types? - natural hx? - most common complication? - what do we call it when there are multiple lesions, but limited to skin? - not limited to skin? |
Hemangioma
- no - females, caucasian, and pre-term infants. - proliferation --> involution - superficial, deep, mixed - reach max size by one year, 90% will resolve by age 9 - ulceration (most common in lip and perineum) - benign neonatal hemangiomatosis - disseminated neonatal hemangiomatosis. |
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Lumbosacral hemangiomas are potential markers of what?
- next step? |
dysraphism
- MRI/CT. |
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Large Segmental Facial Hemangiomas can be associated with which syndromes?
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PHACES syndrome:
- Posterior fossa defects - Hemangioma - Arterial anomalies - Cardiac anomalies (coarctation) - Eye anomalies (micropthalmia, cataracts) - Sternal defects (clefting) |
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What do you do to tx hemangiomas that are life threatening? (2)
How do you tx a hemangioma that is ulcerated, disfiguring, or large proliferating? If surgery is needed, should it be done sooner or later? |
interferon alpha, vincristine (maybe surgery too)
Use topical care (antibxd), Systemic steroids do it earlier. |
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what tx stops the proliferation of most hemangiomas?
- what will proliferation leave if not tx'ed? |
steroids
- residual disfigurement |
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Do arterovenous malformations have a proliferation phase?
- how do they grow? - what is the name given to a capillary malformation? + congenital? + type of borders? + bilateral? + appearance in adulthood? + tx? |
no.
- grow as patient grows - Port wine stain + yes + discrete/irregular + no, unilateral + purple/plaque like + pulsed dye laser (mult tx) |
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Are all PWS benign or are there potential bad associations?
- % of kids with this? - sign of it on radiographic eval? |
Facial PWS along the opthalmic (V1) distribution can be a sign of Sturge-Weber Syndrome.
- Leptomeningeal vascular malfomations (seizures and mental retardation) - ocular choroid (glaucoma) <10% of kids with ophthalmic PWS have SWsx. - tram-track calcifications on meninges. |
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What name do we give to congenital, deep purple lobulated, progresive lesions?
- permanent? - enlarges with...? - painful? |
Venous malformations
- yes - dependency and exertion - painful |
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What do we call congenital lesions of variable size that have a palpable thrill, possible audible bruit, and that are pulsatile and warm?
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arterial-venous malformation
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Klippel-Trenaunay syndrome, Parkes-Weber Syndrome, Proteus syndrome... all are what type of malformations?
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combination of vascular and lymphatic malformations (complex)
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What is Klippel-Trenaunay syndrome?
- what is seen re: bone & soft tiss? |
Extremity PWS w/ underlying complex (venous/lymphatic) malformations.
- hypertrophy of these tissues. |
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In which syndrome do you see MASSIVE, disproportionate, and progressive growth along with PWS & venous/lymphatic malformations?
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proteus syndrome
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