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9 Cards in this Set
- Front
- Back
What are the electolyte characteristics of the sweat of patients with cystic fibrosis?
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sweat is rich in sodium, potassium, and chloride which is typically greater than 60mEq/L
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What are the general lung characteristics in patients with cystic fibrosis?
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pulmonary fibrosis and restrictive lung disease with thick mucous secretion from exocrine glands
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What are the pulmonary problems in patients with cystic fibrosis?
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thick secretions, infection, increased airway resistance predispose to:
1. atelectasis, 2. empyema, 3. abcess formation, 4. pna, 5. ptx, 6. COPD, 7. cor pulmonale (patients have wheezing and decreased pulmonary compliance |
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What GI problems can be encountered in patients with cystic fibrosis?
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1. pancreatic duct obstruction - leads to vitamin deficiency and malnutrition
-(vit A def leads to increased intracranial pressure, -vit E leads to hemolysis and short red cell life), 2. biliary tract obstuction leads to poor absorption of vit K and therefore abnormal hemostasis 3. mucous in the gut can lead to intestinal obstruction |
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What preop testing should you consider in a patient with cystic fibrosis?
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1. PFTs and ABGs,
2. PT/PT - (provide info for biliary obstruction, 3. EKG with special attention to p waves (look for evidence of cor pulmonale) |
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What preop medication should you consider in patients with cystic fibrosis and why?
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atropine - decreases secretions, is anti-vagal, and a bronchodilator
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Why should you be cautious about using N2O in patients with cystic fibrosis?
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should be avoided if there is significant cor pulmonale or large pulmonic blebs
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What are the benefits of volatile anesthetics in patients with cystic fibrosis?
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bronchodilators
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What is the genetics of cystic fibrosis?
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autosomal recessive disease
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