Bb Cystic Fibrosis

Front 1

What are the electolyte characteristics of the sweat of patients with cystic fibrosis?

Back 1

sweat is rich in sodium, potassium, and chloride which is typically greater than 60mEq/L

Front 2

What are the general lung characteristics in patients with cystic fibrosis?

Back 2

pulmonary fibrosis and restrictive lung disease

Front 3

What are the pulmonary problems in patients with cystic fibrosis?

Back 3

thick secretions, infection, increased airway resistance lead to predispose to atelectasis, empyema, abcess formation, pna, ptx, COPD, cor pulmonale(patients have wheezing and decreased pulmonary compliance

Front 4

What GI problems can be encountered in patients with cystic fibrosis?

Back 4

pancreatic duct obstruction leads to vitamin deficiency and malnutrition(vit A def leads to increased intracranial pressure, vit E leads to hemolysis and short red cell life), biliary tract obstuction leads to poor absorption of vit K, mucous in the gut can lead to intestinal obstruction

Front 5

What preop testing should you consider in a patient with cystic fibrosis?

Back 5

PFTs, ABGs, PT/PTT(provide info for biliary obstruction, EKG with special attention to p waves(look for evidence of cor pulmonale)

Front 6

What preop medication should you consider in patients with cystic fibrosis and why?

Back 6

atropine(decreases secretions, is anti-vagal, and a bronchodilator)

Front 7

Why should you be cautious about using N2O in patients with cystic fibrosis?

Back 7

should be avoided if there is significant cor pulmonale or large pulmonic blebs

Front 8

What are the benefits of volatile anesthetics in patients with cystic fibrosis?

Back 8

bronchodilators