Reading...
Play button
Play button
Use LEFT and RIGHT arrow keys to navigate between flashcards;
Use UP and DOWN arrow keys to flip the card;
H to show hint;
A reads text to speech;
16 Cards in this Set
- Front
- Back
|
A genetic disorder that causes CNS damage from toxic levels of the amino acid phenylalanine in the blood is ?/? This is caused by a deficiency of the liver enzyme ? which is necessary to convert phenylalanine to ? for use. It is an ? recessive disorder, which means that the abnormal gene must be passed to the child from ? parents.
|
Phenylketonuria/hyperphenylalaninemia
Phenylalanine hydrolase, tyrosine, autosomal, both |
|
|
Severe ?,?,? disability occurs in untreated infants and children that have the autosomal recessive disorder PKU. In the U.S. all infants are ?'d for PKU prior to D/C because ? counts. The infant must begin ? before the PKU test can be performed to ensure that enough ? is consumed for the test to be accurate.
|
mental, physical, behavioral,
screened, time, feeding, protein |
|
|
Blood PKU levels greater than ?mg/dl are abnormal. A normal PKU level is <?mg/dl 2-5 days after birth.
|
8mg/dl,
2mg/dl |
|
|
If an infant is found to have a PKU abnormality it will be placed on a low ? diet for ? What not to eat: High protein foods such as ? products, ?,?,?,?,?,? and NO ?
|
phenylalanine, life,
dairy, meat, chicken, fish, eggs, beans, nuts, Aspartame |
|
|
What can the infant with PKU eat: ?,?,?,?, and a special phenylalanine-? formula, that contains vitamins, minerals and specific acceptable ?'s. The RN should stress the importance of close ?-?, and need for nutritional consult.
|
Fruit, Vegetables, bread, pasta,
phenylalanine-free, proteins, follow-up |
|
|
Nursing Dx for PKU: Altered ? r/t low ? diet.
|
nutrition,
phenylalanine |
|
|
Drug abuse during the ? trimester may cause congenital defects. Later abuse may interfere with development or functioning of ? already formed. Abuse of more than one substance is common, making it more difficult to determine which ? led to the individual deffect.
|
1st,
organs, substance |
|
|
With drawal signs from prenatal drug exposure can start from ?-? hrs after birth and even less for alcohol exposed neonates ?-? hrs.
|
48-72hrs,
3-12hsr |
|
|
WITHDRAWAL SUCS acronym stands for ?
|
W=wakefulness, I=irritability, T=Tremulousness,
H=hyperactivity, D=diarrhea, R=Rub marks, A=Apnea, W=weight loss, A=alkalosis, L=lacrimation. S=Seizures, U=uncoordinated suck, C=Cry-high pitched, S=super moro |
|
|
Nursing mgmt for neonate with prenatal drug exposure: ? drug screen or ? screen. Withdrawal may be confused with ?,?, or ? disorders so testing may be done to rule these out. Drug therapy can include ?, oral ?, tincture of ?, ?, or ?
|
urine, meconium,
sepsis, hypoglycemia, neurological, phenobarbital, morphine, opium, methadone, diazepam |
|
|
Nursing mgmt for neonate with prenatal drug exposure continued: May require assistance with feeding such as ? or ? feeding. Some infants need more than the normal ? requirements b/c of their excessive ?
|
gavage, IV,
caloric, activity |
|
|
Nursing mgmt for neonate with prenatal drug exposure continued: Minimize ? keep the infant in a ? environment. Provide comfort measures such as ?,?,? The RN should assess for ? between parent and infant. The infant may require ? care.
|
stimulation, quiet,
swaddling, pacifier, rocking, bonding, foster |
|
|
What types of signs would the RN who is assessing a pregnant woman look for if drug abuse is suspectcted: A hx of minimal or no ? care, watch the mothers ? during labor. Placental abruption may occur after ? use. If there is drug abuse suspected the infant is observed ? for S/S of prenatal drug abuse.
|
prenatal,
behavior, Cocaine, closely |
|
|
When an infant tests positive for drugs ?-?-? becomes involved.
|
child-protective-services
|
|
|
NIPS(Newborn Infant Pain Scale): The RN is looking at facial ?s, ?-pattern,?,?,?, and state of ? to measure the pain level of the infant. This Scale if from 0-2 with ? being normal activity and ? showing S/S of irritability and ? being a loud schrill scream or a ? cry if intubated (aeb facial expression).
|
expressions,
breathing, legs, arms, cry, arousal. zero, one, two, silent |
|
|
Nsg Dx for Infant withdrawal: Altered ? less than body requirements r/t abnormal ? and ? and excessive ?
|
nutrition,
suck, swallow, activity |
