Branched-chain amino acids

Maple Syrup Urine Disease (MSUD) is a rare, autosomal recessive metabolic disorder in which the body is unable to process certain amino acids properly. It causes brain damage and progressive nervous system degeneration. MSUD is caused by mutations in three different genes: BCKDHA, BCKDHB and DBT (Warrell, Cox and Firth, 2012). The BCKDHA gene causes MSUD Type Ia due to the mutation in the E1α subunit, BCKDHB causes Type Ib due to the mutation in the E1ᵦ subunit, and DBT causes Type II due to…

the scenes directors for the nutrients you consume. Without an adequate supply of multivitamins, any other supplement you take will be working below its potential. BCAA's (Branched Chain Amino Acids) Branched chain amino acids are critical. They function in promoting protein synthesis and helping transport other amino acids into the muscles for growth and repair. Our bodies cannot produce BCAA's so we must take them into our bodies. The usual source for them is dietary protein. Intense…

Maple Syrup Urine Disease (MSUD) is a rare, potentially deadly disorder where the body cannot break down the three branched- chained amino acids (BCCA): leucine, isoleucine and valine. These amino acids are used to build proteins and when they are not being used they can be broken down and recycled in the cell. The complex that breaks these amino acids down is called BCKD (branched-chain alpa-ketoacid dehydrogenase) and is made up of six proteins. When a person has a mutation in one of the six…

fatty acids: Synthesis of fatty acids take place in the crystal. The enzymes of fatty acid synthesis are wrapped in a complex called fatty acid synthase(FAS). At a time 2 carbons are synthesized by fatty acid molecule.Palmitic acid is the product…

Amino acids support intracellular nitrogen retention levels for faster muscle growth and strength increases.Over 9,000mg of BCAA’s (Branched Chain Amino Acids) BCAA’s have an anti-catabolic effect (prevents muscle tissue breakdown)Over 10,000mg of Glutamine & Glutamic Acid. Studies show that supplemental glutamine can also prevent muscle breakdown.35 grams of Whole Carb Whole Food Carbohydrate…

how to gain muscle weight fast due to its Omega-3 fatty acid content. This works by making your system more sensitive to insulin to fuel storage of glycogen and amino acids going into your body while storing your glutamines. 2. Add in more sodium in your diet. Well, there are not many people who know that sodium is important on how to gain muscle weight fast. It enhances your capacity to store carbohydrates and ability to absorb more amino acids. In addition, it also makes…

roughly 10% comprised of essential fatty acids, and carbohydrates with 20-35% fiber, but lower in protein by up to 50%. It is a great protein option for individuals who have an allergic reaction to animal proteins. Hemp Protein Benefits The popularity of hemp protein lends partly to the fact that it contains two proteins-albumin and edestin, which comprises of a group of essential amino acids, which the human body requires but does not produce. Amino acids are essential to fueling the…

performance. "True Hydration" reduces cramping and increases power throughout strenuous activity, giving you maximum physical benefits. The addition of Branched Chain Amino Acids supports muscle function, growth and recovery. BCAA loading while training keeps muscles primed and avoids muscle atrophy that comes from overexertion without proper feeding. Amino Hydrates unique combination assists athletes in performing at their peak longer, without post training exhaustion. it's a lower…

Background In 2014, the American Association for the Study of Liver Diseases (AASLD) and European Association for the Study of the Liver (EASL) published a new set of practice guidelines for Hepatic Encephalopathy (Vistrup et al., 2014). These guidelines define Hepatic Encephalopathy (HE) as “a brain dysfunction caused by liver insufficiency and/or portosystemic shunting, and manifests as a wide spectrum of neurological/psychiatric abnormalities ranging from subclinical alterations to coma”…

Laforin is a 331 amino acid protein with a carbohydrate-binding domain (CBD) at its amino terminus. This CBD allows the protein to bind to glycogen and Lafora bodies, with preference given to the latter. Recent studies suggest that the binding of the CBD of laforin to Lafora bodies may be involved in the…