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4 Cards in this Set
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- Back
- 3rd side (hint)
Granulomatosis with Polyangitis |
Wegener granulomatosis Necrotizing granulomas *U and L respiratory tract *Granulomatous vasculitis (pulmonary V) *Crescentric glomerulonephritis C-ANCA/PR3-ANCA FEATURES:persistent pneumonitis, nasopharyngeal ulcers,Renal disease Treatment: Steroids Cyclophosphamide |
C disease |
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Microscopic polyangitis |
#Leukocytoclastic vasculitis (pauci immune injury) #All lesions same age unlike PAN #Unlike Wegeners no nasopharynx and granulomas(necrotizing pulmonary vasculitis and glomerulonephritis are similar) #P-ANCA/MPO-ANCA #FEATURES: depends on vascular bed Hemoptysis, hematuria,protenuria, bowel pain |
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Churg Strauss Syndrome |
#Associated with Asthma, Allergic rhinitis lung infiltration #Hypereosinophilia(Allergic vasculitis) #Extravascular necrotizing granulomatosis #P-ANCA #FEATURES: Palpable purpura,GI bleeding,Heart(Cardiomyopathy) |
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Henoch Schölein purpura |
#IgA immune complex deposition #Most common pediatric vasculitis #Visible purpura-Buttoks and legs #IgA nephropathy -hematuria #associated with PAN |
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