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37 Cards in this Set
- Front
- Back
What are the Rheumatic Diseases of kids that I need to know?
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Juvenile Idiotpathic Arthritis (JIA)
Systemic Lupus Erythematous (SLE) Juvenile Dermatomyositis (JDM) Kawasaki Disease (KD) |
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Which is the most common rheumatic disease of kids?
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JIA
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Criteria for JIA Dx?
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Under 16yrs old
Arthritis in 1 or more joints Lasts for at least 6 weeks Exclusion of other causes (infection, malignancy, etc) |
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How is arthritis defined for kids?
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Swelling
Effusion Warmth Limited Movement |
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Types of JIA?
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Systemic
OligoA PolyA Psoriatic A Enthesitis-related A |
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What is common with Systemic JIA?
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A rash that comes and go with fever
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What are other extra articular manifestations of JIA?
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Fever
Rash Uveitis Lymphadenopathy Hepatosplenomegaly Pleuritis Nodules Pericarditis Abd Pain |
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Difference in number of joints involved between polyarticular and oligoarticular?
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Poly = 5
Oligo = 4 |
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Gender and JIA?
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Females more than males except in Systemic where they're =
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When do you usually see uveitis?
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Oligoarticular JIA (20%)
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When are kids Rheumatoid Factor Positive?
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10% of polyarticular and increases as they age
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Who has ANA's?
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Poly (50%)
Oligo (75%) Systemic (10%) |
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Who has a bad prognosis?
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Just systemic
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Rx of JIA?
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Arrest Inflammation
Treat Extra-articular manifestations Maintain normal G&D Prevent Deformities |
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How many JIA pts have arthritis in adulthood?
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30-40%
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Who has the best prognosis?
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Pauciarticular JIA
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how much SLE begins in childhood?
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15%
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Typical Sx's of SLE in kids?
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Rash
Arthritis Pleuritis Anemia |
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Constitutional Sx's at onset of JSLE?
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Fatigue
Fever Wt Loss |
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SLE Lab Tests
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CBC, WSR, Coombs
Liver Enzymes, CPK Urinalysis ANA, Anti DNA Ab, anti Sm Ab C' C3, C4 |
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Sx's of Neonatal Lupus and their duration
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Congenital Heart Block (permanent, rest are transient)
Dermatitis Thrombocytopenia Neutropenia Hepatitis |
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Rx of SLE?
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Steroids (corticosteroids)
Lots of other stuff |
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Etiology of Juvenile Dermatomyositis?
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Infection: (flu, coxsackie, myxo, parvo B19, toxo)
Immunodeficiency |
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Sx's of JDM?
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Progressive, Symmetric weakness of Proximal Muscles (limbs, abs, neck flexors)
Skin Rash (eyelids, gottron's papules, extensor surface of elbows, knees, etc) Calcinosis |
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Dx of JDM?
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Muscle Enzymes
ANA and other autoAb's MRI Muscle Biopsy |
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Rx of JDM?
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Corticosteroids
PT |
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Prognosis of JDM?
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Full Recovery in 2yrs
Course w/ remission and relapses or Chronic, Unremitting course w/ calcinosis |
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Other name for Kawasaki's?
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Mucocutaneous Lymph Node Syndrome
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Loose Definition of KD?
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Systemic vasculitis of small and medium arteries
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Dx Criteria for KD?
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Fever
Conjunctivitis LN Enlargement Rash Changes of Lips and Mucosa (strawberry tongue) Erythema, Edema, and Desquamation of hands and feet |
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Other possible Sx's of KD?
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Irritable
Meningitis Arthritis Gallbladder Hydrops Diarrhea Urethritis Uveitis Pneumonitis Lots with CV system |
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Two kickers to look for w/ testing?
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Platelet Count
Coronary Artery Dilation (cause these can F you up) |
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Rx for KD?
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High Dose NSAIDs or aspirin
IV Gammaglobulin |
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What do you need to watch out for in the long run with KD?
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Aneurysms
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What is another condition that causes rheumatic complaints, but without inflammation and altered immune status?
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Benign Hypermobility Syndrome
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Epidemiology of BHS?
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8-15% of kids
Girls>Boys |
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Sx's of BHS?
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Arthralgias
Knees>Elbows>ankles TMJ Pain Pain w/ excessive activity |