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19 Cards in this Set
- Front
- Back
PROPHYLACTIC THERAPY IS USED TO__
-STARTED AT AGE__ -FACTOR GIVEN__ |
TO KEEP FACTOR LEVEL > 1
-START AT AGE 1-2 YRS -FACTOR VIII TIW -FACTOR IX BIW -IVAD |
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PT SHOULD BE VACCINATED AGAINST__
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1.HEPATITIS B
2.PT STILL AT RISK FOR HEP C |
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OTHER NSG MEASURES FOR HEMOPHILIA
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-NO IM (ONLY SUB Q)
-GOOD DENTAL CARE -CHECK TYPE OF SHOES -MED ALERT ID 1.COSTLY DISEASE 2.NEED COMPREHENSIVE TEAM APPROACH 3.GENETIC COUNSELING 4.GENE THERAPY IN PROCESS 5.PROPHYLACTIC THERAPY |
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NSG PLAN/IMPLEMENT FOR HEMOPHILIA
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A.GROWTH AND DEVELOPMENT
-AVOID OVERPROTECTING -ALLOW CHILD TO RUN,EXPLORE,CLIMB -NEED REGULAR PROGRAM OF EXERCISE,SELF ESTEEM B.BLEEDING EPISODE -ADMINISTER**FACTOR A OR B CONCENTRATE IV (AHF=ANTIHEMOPHILIC FACTOR) -(9-12 YRS OLD=SELF ADMINISTRATION) -**CRYOPRECIPITATE NO LONGER RECOMMEND |
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NURSING FOR MINOR CUT
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TREAT SAME AS WOULD FOR ANYONE ELSE
-APPLY PRESSURE Q 10-15 MIN -INCREASE EXTREMITY -IMMOBILIZE -COLD PACKS |
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NSG DIAGNOSIS FOR HEMOPHILIA
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1.RISK FOR INJURY
2.KNOWLEDGE DEFICIT 3.INEFFECTIVE COPING |
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LAB TEST
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1.STAGE 1 (PTT)
CHECK HEPARIN 2.STAGE 2 (PT) CHECK COUMADIN FACTOR ASSAY PROCEDURE |
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IF HEMOPHILIA MILD,DIAGNOSE__
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DELAYED, POST-OP
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IF HEMOPHILIA SEVERE,DIAGNOSIS MADE DURING __
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INFANT/TODDLER
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ASSESSMENT
HISTORY P.E. |
HISTORY-HEMOPHILIA IS A GENETIC D/O
FAMILY HISTORY HISTORY OF PROLONGED BLEEDING P.E.:1.VS,SKIN COLOR,TEMP,DYSPNEA 2.JOINT SWELLING 3.BRUISES |
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MAJOR CONCERN
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HEMARTHROSIS(BLEEDING IN THE JOINTS)
S/S:TINGLING,BUBBLING SENSATION,CAN BE SPONTANEOUS JOILT TWIST -JOINT WILL BE DAMAGED AND SURGERY NEEDED.JOINT WILL SWELL W/BLD AND GET STIFF.TISSUE WILL BE DESTROYED-->ANKYLOSIS |
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HEMARTHROSIS CAN LEAD TO__
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ANKYLOSIS
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SEVERITY OF HEMOPHILIA DEPENDENT ON__
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AMT OF FACTOR PRESENT
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CHRISTMAS DISEASE
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FACTOR IX IS DEFICIENT
AKA: HEMOPHILIA B -AFFECTS 2ND PHASE OF 1ST STAGE IN COAGULATION PROCESS(THROMBOPLASTIN) |
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WHAT SHOULD PT BE CONCERNED W/ HEMOPHILIA
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INTERNAL BLEEDING
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WHAT HAPPENS TO BLEEDING W/ HEMOPHILIA
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BLEEDING IS PROLONGED
WHY?BECAUSE NO CLOTTING FACTOR NOT:EXCESSIVE BLEEDING,NOT PROFUSE BLEEDING,NOT FASTER BLEEDING |
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CLASSIC HEMOPHILIA
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FACOR VIII IS DEFICIENT
AKA: HEMOPHILIA A |
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VON WILLEBRAND
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MALE AND FEMALE
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HEMOPHILIA
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INHERITED D/O OF BLOOD CLOTTING
- X LINKED RECESSIVE=MALE - CARRIERS FEMALE=ASYMPTOMATIC |