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26 Cards in this Set

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Impaired / Decreased platelet count

BERNARD-SOULIER syndrome


Fanconi anemia


TAR syndrome


Viral infection


Leukemia


Megaloblastic anemia


WISKOTT-ALDRICH syndrome


MAY-HEGGLIN ANOMALY

increased platelet destruction

HUS


DIC


ITP


TTP


HIT

Increased splenic sequestration

gaucher disease


hodgkin disease


sarcoidosis


lymphoma


cirrhosis of liver


portal hypertension

Reactive lymphocytosis other name

secondary thrombocytosis

Autonomous thrombocytosis other name

primary thrombocytosis

autonomous thrombocytosis example of associated diseases

Essential thrombocythemia


Chronic myelogenous leukemia


Polycythemia vera


Primary myelofibrosis

EC PP (easy pp)

Platelet adhesion disoders

Bernard soulier syndrome


von Willebrand disease

Platelet aggregation disoder

Glanzmann's thrombasthenia

Platelet secretion disorder

Thromboxane pathway disorder

deficiency of GP 1b/IX/V

Bernard soulier syndrome

Platelet receptor for vWF

GP 1b/IX/V

Normal aggregation with



ADP


Collagen


Epinephrine

Bernard soulier syndrome


vWD

Abnormal aggregation with restocetin

Bernard soulier syndrome

most common vWD, mild bleeding tendencies

type 1

most severe in bleeding tendencies type of vWD, rarest type

type 3

Platelet fibrinogen receptor

GP IIb/IIIa

Abnormal aggregation response in ACE

glazmann thrombasthenia

normal aggregation in restocetin

Glazmann thrombasthenia

Alpha granules deficiency

gray platelet syndrome

dense granule deficiencies

hemansky-pudak


chediak-higashi syndrome


TAR syndrome


Wiskott-aldrich syndrome

basta gwapo dense na sila

X-linked recessive inheritance

wiskott-aldrich syndrome

gradual increase from low platelet until normal in adult (1 year old)

TAR syndrome

Oculocutaneous albinism

Hermansky-pudlak syndrome

Partial albinism

Chediak-higashi syndrome

deficiency of GP IIb/IIIa


autosomal recessive

Glanzmann's thrombobasthenia

Increase BT


Abnormal clot retraction

Glanzmann thrombasthenia