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389 Cards in this Set

  • Front
  • Back

The ______ is at a right angle to the AV Valves

PV

In a normal heart the ____ MV leaflet has continuity with the ____ Ao leaflet

Anterior MV






Non-coronary Ao cusp leaflet

In D-TGA, the PDA flow is into the PA and should be______.

Left to right

IAA


A-


B-


C-

A-beyond the LSCA (left subclavian)




B- Between LSCA and LCC (most common)




C-Between LCC and innominate

Most IAA have a _____

VSD

Rastelli type A common AV Valve

The superior bridging leaflet is almost completely adherent to the left ventricle and is firmly attached on the  the ventricular septum by multiple chordal insertions

The superior bridging leaflet is almost completely adherent to the left ventricle and is firmly attached on the the ventricular septum by multiple chordal insertions

Rastelli type B common AV

The superior bridging leaflet is attached over the ventricular septum by an anomalous papillary muscle of the RV

Rastelli type C (AV Common)

The superior bridging leaflet is not attached to the ventricular septum (free floating leaflet)



Days 0-20

No heart or great vessels

Day 20

Vascular tubes

Day 23

First (ineffective) contractions


aka the heart beats!

Day 24

Bulboventricular looping

Day 27

Muscular septum cushions appear

Day 31

Fusion of truncus swellings

Day 34

Septation: Fusion of conus and endocardial cushions

Day 40

Final cusion formation AV Valve cusps

Common defect in kids born to moms with lupus

Heart Block

An AVSD would be fully formed at ___ fetal days

30-40

VSD V= 4m/s


SBP= 104


PAP=?

40 mmHg

Atrio-ventricular connection


1)


2)


3)

1 Normal


2 inverted


3 double inlet ventricle

VSD is ______


sytolic/diastolic?

systolic

AVSD is the result or arrest of development of the heart at ________ days gestation

33 days

AVSD is associated with:

Downs Syndrome/ trisomy 21

CVP

Central venous pressure


4v2 +cvp (5 or 10 mmHg)

With _______the heart is turned to the right so the LV is in front and RV in back. (not mirror image)

dextroversion

Types of pulmonary venous connections


A)


B)

A) Normal


B) Anomalous -total or partial

D TGA

S1

MV and RV CLOSURE

Basic Cardiac Position


A


B


C

A Levocardia


B Dextrocardia


C Mesocardia

Malalignment VSD is seen in


1


2


3



1 TOF


2 Trucus


3 DORV


all can be cyanotic



L TGA

AVSD is also called: (2 THINGS)



1. complete AVSD canal defect


2. Endocardial cushion defect

An ostium primum ASD and inlet VSD is called?

AVSD

Partial AVSD is either (2 THINGS)


1. Ostium primum ASD plus cleft in anterior MV leaflet or septal TV Leaflet


2. Inlet VSD and cleft of MV or TV

Classic VSD Echo features (3 THINGS)



1. LA dilation


2 LV and RV Volume Overload


3 Normal septal motion

Most anterior part of heart in dextroversion is the_______

LA

S1


S2


S3


S4

S1 AV CLOSE


S2 SEMI-LUNAR CLOSE


S3 VENT FILLING


S4 ATRIAL CONTRACTION

THE S1 AND S2 HEART SOUNDS ARE GENERATED BY VALVE___________

CLOSURE

DORV

DEXTROVERSION MEANS TURNED TO THE________

RIGHT

IAA IS A _____ ________LESION

DUCTAL DEPENDENT, R->L

DTGA FIX=

JATENE+LE COMPTE +CORNOARY BUTTONS

WITH MS, YOU GET________ENLARGEMENT

LEFT ATRIAL

NORMAL MV AREA

4-6CM2

THE____ THE PRESSURE 1/2 TIME, THE SMALLER THE VALVE AREA= MORE STENOTIC

HIGHER

THE TIME IT TAKES FOR THE TRANSMITRAL PRESSURE GRADIENT TO DECREASE BY HALF=

MV PRESSURE 1/2 TIME

A SUPRAVALVULAR MITRAL RING IS CLOSER TO THE _______THAN THE ______


COR TRIATIATUM IS PROXIMAL TO THE ______

MV


LAA


LAA

THE MOST COMMON CORONARY IN TOF IS A ______

BIFURCATED RCA RATHER THAN LEFT MAIN

HIGH PULMOARY BLOOD FLOW:


1


2


3



1 TGA


2 TRUNCUS


3 TAPVR

IN FETAL CIRCULATION THE ABSOLUTE HIGHEST O2 CONTENT IS THE ______

UMBILICAL VEIN

LTGA IS ASSOCIATED WITH _________

HEART BLOCK

NORMALS (CO,HR.SV) FOR A NEWBORN=

CO= 700-800 ML/MIN


HR= 145 BPM


SV=5ML

FOR A SUBAORTIC (DISCRETE) MEMBRANE,


REPORT:

PEAK GRADIENT

PULMONARY ATRESIA

AN ATRIAL SEPTOSTOMY IS NEEDED WHEN THE ASD VELOCITY IS >________

1 M/S

MOST COMMON CARDIAC TUMOR IN CHILDHOOD

RHABDOMYOMA

WHICH OF THESE IS NOT IN KAWASAKI'S DISEASE?




1) PEELING HANDS AND FEET


2) COARTCT ANEURYSMS


3) FEVER


4) AI


5) LARGE OCCIPITAL LYMPH NODES

4) AI

MAX DIAMETER OF NORMAL LM AND RCA IN A 1 YEAR OLD

3 MM

TRUNCUS TYPE IV

PA FROM DESC AO

BT SHUNT=

SUBCLAVIAN OR CAROTID TO PA

IN TOF THERE USUALLY IS A PROMINENT _____ ___________ FROM THE RCA OVER THE RVOT

CONAL BRANCH

RHABDOMYOMA IS WITHIN THE _______

MYOCARDIUM (TUBEROUS SCLEROSIS)

TUBULAR SCLEROSIS

The primary cardiac finding in people with the tuberous sclerosiscomplex (TSC) is the presence of rhabdomyomas. These are non-malignant (or non-cancerous) tumors that can occur anywhere in the heart, but most commonly occur in the ventricular and septal walls

MUCOCUTANEOUS LYMPH NODE SYNDROME

KAWASAKI

IF YOU SEE DILATED CM, CHECK FOR_____

ALCAPA Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA)

TAMPONADE=

ATRIAL VENTRICULAR COLLAPSE IN DIASTOLE

POLYSPLENIA CAUSES:

TWO LEFT SIDES

ASPLENIA CAUSES:

TWO RIGHT SIDES

PERSISTENT FETAL CIRCULATION=


MOST COMMON

MECONIUM ASPIRATION

IF YOU SEE AN INFANT W/ SEVERE PI, THINK OF

ABSENT PV SYNDROME

EISENMENGERS IS COMMON IN

T21 DOWN SYNDROME

CENTRAL SHUNT IS

ASCENDING AO TO RPA

DUCHENNE IS ASSOCIATED WITH _______CARDIOMYOPATHY

RESTRICTIVE

DIGEORGE LESIONS


1


2


3


4

1 IAA


2 TRUCUS


3 TOF


4 DORV

DIGEORGE KIDS HAVE NO________

THYMUS

NEWBORN IN CHF WITH LOWER FUNCTION


RULE OUT:

Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA)

ACUTE RHEUMATIC FEVER DOES NOT INCLUDE

MS (TOO LONG STANDING)

DEXTRO ANOMALOUS SYSTEMIC AND PULMONARY VENOUS RETURN + AVSD +PULMONARY ATRESIA

ASPLENIA SYNDROME

NEWBORN WITH 96% O2 IN RIGHT HAND, 80 %IN RIGHT FOOT:

COULD BE:


COARCT WITH PDA


INTERUPTED


R->L PDA


FEMORAL ART CATH

PERSISTENT FETAL CIRCULATION 2

RIGHT TO LEFT PFO AND PDA

THE 5 TS OF CYANOTIC LESIONS + 2

1 TGA


2 TOF


3 TRUNCUS


4 TRICUSPID ATRESIA


5 TAPVR


DORV


HLHS

YOU WOULD NEVER WANT TO CLOSE ________IN HLHS

AN ASD OR PDA

25% OF EBSTEINS HAVE ________ OR __________.

WPW OR PAROXYSMAL ATRIAL-TACHY

50%OF EBSTEINS CASES HAVE A ________

ASD

IN HLHS THERE SHOULD BE A LARGE _____ TO _________ ______________

RIGHT TO LEFT PDA

MARFANS, EHLERS-DANLOS CUTIS LAXA=

AO DILATION MVP

WALL MOTION SCORING

1 NORMAL


2 HYPOKINESIS


3 AKINESIS


4 DYSKINESIS


5 ANEURYSMAL

WILLIAMS TRAITS



UPTURNED NOSE LONG UPPER LIP

FETAL ALCOHOL SYNDROME CAUSES

VSD

A ______IS MANDATORY IN DORV

VSD

AN AP WINDOW IS A _____TO ______SHUNT

LEFT TO RIGHT

T18 LESIONS and traits

#1 VSD


CLEFT LIP


LOW EARS


ROCKER BOTTOM FEET


CLENCHED HANDS

INITIATES THE HEART BEAT FROM THE SA NODE CAUSING ATRIAL CONTRACTION SYSTOLE

P WAVE

INITIATES VENTRICULAR SYSTOLE CONTRACTION:

QRS COMPLEX

GLENN=

SVC TO R AND LEFT PAs

AN OSTIUM SECUNDUM ASD IS AT THE

FOSSA OVALIS

DORV IS CLASSIFIED BY WHERE THE _____IS

VSD

BULBO VENTRICULAR LOOP


1


2

DEXTRO NORMAL RV ON RIGHT


LEVO RV ON LEFT "L FOR LEVO"

INDICATES VENTRICULAR RECOVERY AND OCCURS DURING LATE VENTRICULAR CONTRACTION

T WAVE

DELTA WAVE ON ECG

WOLF PARKINSON WHITE GOES WITH EBSTEINS

SANO=

RV TO PA SHUNT



HLHS SURGERIES


1


2


3

1. NORWOOD


2. GLENN


3. FONTAN

EARLIEST FORM OF ECHO

BATS JUST KIDDING


MMODE WAIT NOT B MODE?

TIME MOTION MODE=

M MODE

LA/AO RATIO=NORMAL ON M MODE

<1.2

2D IMAGING IS ALSO CALLED


1


2A


2B

1 MULTISCAN


2A SECTOR SCAN MECHANICAL


2B PHASED ARRAY

TURNER SYNDROME IS MOST LIKELY ASSOCIATED WITH ___________.

COARCTATION OF AORTA AND BICUSPID VALVE

MOST TRISOMIES 13,18,21 Have_________

VSDs

HOLT-ORAM LESION

ASD ORAM PUTS THE A IN ASD

ELLIS-VAN CREVALD TRAITS


1


2

1 ASSOCIATED WITH AMISH


2 DWARVES

WITH AN ASD IT IS TYPICAL TO SEE INCREASED

FLOW ACROSS THE PULMONARY VALVE

THE MOST COMMON ASSOCIATED LESION WITH TOF________

RAA

YOU WOULD SEE A PFO STRETCH WITH THESE TWO ADDITIONAL DEFECTS

PDA AND VSD

CONTINUOUS MURMUR

PDA

DKS


SANO


PROCEDURES

HYPOPLASTIC LEFT HEART SYNDROME

A PFO IS USUALLY ____ TO ____MM IN SIZE AND CAN STRETCH

2-3 MM

ELLIS VAN CREVALD THINK=

THE AMISH HAVE ASDs

DORV TYPES 1-4

I VSD RELATED TO AO


II VSD RELATED TO PV


III VSD TO BOTH


IV VSD TO NEITHER



IN TRUNCUS, IF THE SEMI-LUNAR VALVE IS COMPETANT THAN A ________IS PERFORMED

RASTELLI


RV TO PA CONDUIT

ATRIAL SEPTATION FETAL OCCURS AT DAYS

27-40

A CORONARY SINUS ASD IS ALSO CALLED

UNROOFED CORONARY SINUS


FLOW CS TO LA

A CAVAL ASD IS ALSO CALLED

INFERIOR SINUS VENOSUS

IF THERE IS NO_______IN TRICUSPID ATRESIA, THEN THERE MUST BE A PDA

VSD

TURNER LESIONS (2 THINGS)



CORAC, BI AO STENOSIS

MOST COMMON ASSOCIATED LESION WITH T 21

AVSD OR ENDOCARDIAL CUSION DEFFECT

IN TRICUSPID ATRESIA THER MUST BE A ________TO __________ ________

RIGHT TO LEFT SHUNT

TGA AORTIC VALVE AND RV LIE TO THE LEFT

L TGA ANATOMICALLY CORRECTED


ACYANOTIC

TURNERS THINK

TURN AROUND THE AORTA

L= ______ IN LTGA

LEVO

THE FAILURE OF SPIRALIZATION OF THE TRUNCUS SEPTUM

D-TGA

T13 PATAU TRAITS


4

1CLEFT LIP


2 EXTRA DIGITS


3 CLENCHED HANDS


4 WIDE NIPPLES


CONNECTS THE MPA TO THE AORTA THE FAULTY AORTA IS OVESEWN AND RV CONDUIT

DKS

WHEN THE PLACENTA IS REMOVED, THE _______CIRCULATION RESISTANCE INCREASES AND ______ _____CLOSES

SYSTEMIC,


DUCTUS VENOSUS

IN HYPOPLASTIC LEFT HEART SYNDROME, THE ASCENDING AORTA FUNCTIONS AS

COMMON CORONARY ARTERY

INFINDIBULAR,


CONAL,


SUPRACRISTAL,


SUBPULMONARY,


DOUBLY COMMITTED=

OUTLET

CONTRIBUTES TO THE INLET OF BOTH VENTRICLES AND PRIMARY LV FUNCTION

PRIMATIVE VENTRICLE

CONTRIBUTES TO THE PRIMARY FUNCTION OF THE RV AND OUTFLOW TRACTS:

BULBUS CORDIS

LOW PULMONARY BLOOD FLOW:


4

1 TOF


2 TRICUSPID ATRESIA


3 PULM ATRESIA


4 PERSISTENT FETAL CIRCULATION

SYSTOLIC HEART MURMUR


5

1 AS MID


2 PS MID


3 VSD HOLO


4 MR HOLO


5. TR HOLO

TURNERS SYNDROME TRAITS

SHORT


PUFFY HANDS AND FEET


WEBBED NECK


LOW HAIRLINE

D TGA +VSD+ PS = _______ REPAIR

RASTELLI RV TO PA CONDUIT

THE BEST MEASUREMENT FOR MS IS :

P1/2 T

Noonan trait

ELF LIKE

SMALL=


MOD =


LARGE =


VSD

SMALL<1/3 AO DIAMETER


MOD 1/3-2/3 AO DIAMETER


LARGE >2/3 AO DIAMETER

THE FAILURE OF ABSOPTION OF LEFT CARDINAL VEINS =

ANOMALOUS OR PERSISTENT LSVC

A VASCULAR SLING IS

LPA ORIGINATING FROM RIGHT

VASCLAR RING IS CAUSED BY

ANOMALOUS RSCA

IN DORV IF THE AO AND PA ARE TRANSPOSED

TAUSSIG BING

SV IS DETERMINED BY


3

1 PRELOAD END DIASTOLIC VOL


2 AFTERLOAD RESISTANCE OF SYSTEMIC CIRCULATION BP


3 CONTRACTILITY

WILLIAMS LESIONS

SUPRAVALVULAR AS


WILLIAMS THINK


I I


V V


A S

ECHO GRADIENTS ARE ________AND CATH GRADIENTS ARE ______________

INSTANTANEOUS,


PEAK TO PEAK

DOUBLE INLET VENTRICLE



STRADLING TRICUSPID VALVE

_______ GOES WITH CORARCTATION OF AORTA

BICUSPID AORTIC VALVE

A ______ TO _____ PDA SUGGESTS PULMONARY HYPERTENSION

R -> L

ATRIAL MYOMA IS ______IN CHILDREN

RARE

THE AV VALVES ALWAYS STICK WITH THEIR _____

VENTRICLES

IN TAPVR, A ______SHUNT IS REQUIRED

R->L ASD

TYPES OF TAPVR


4

1 MIXED 2%


2 SUPRACARDIAC 30%


3. CARDIAC 55%


4 INFRACARDIAC 13%



RASHKIND

BALLOON ATRIAL SEPTOSTOMY

A ______ IS NOT A COMPNENT OF THE SHONE COMPLEX

PDA

for diffuse obstruction of an outflow use ____________gradients

mean

ms and ts are ________ or ___________ murmurs

diastolic or presystolic murmurs

_________ sided pressures are lower than __________

RIGHT


LEFT

THERE IS NOT TYPICALLY A ________ IN HYPOPLASTIC LEFT HEART SYNDROME

R-> L

VSD

IN RESTRICTIVE CARDIOMYOPATHY, ________IS NOT COMMON

ASYMMETRIC SEPTAL THICKENING

MALALIGNMENT VSD IS ASSOCIATED WITH

TOF

_______ __________ IS NOT SEEN IN DIGEORGE SYNDROME

COMMON ATRIUM

NORMAL HEMODYNAMICS CHANGE WITH AGE


CO=


HR=


SV=

CO INCREASES


HR DECREASES


STROKE VOLUME INCREASES

A SINUS VENOSUS ASD IS MOST COMMONLY ASSOCIATED WITH

PAPVR (R PULM VEIN)

STRADDLING MITRAL VALVE

CELLS ARE AT DIFFERENT DIRECTIONS AND AT MANY DIFFERENT AND FASTER VELOCITIES

TURBULENT FLOW

ALL CELLS ARE TRAVELING PARALLEL AND AT THE SAME VELOCITY

LAMINAR FLOW

PAPVR IS NOT A _______ LESION

CYANOTIC

UNROOFED CORONARY SINUS IS A ____TO______ SHUNT

L->R

AN UNROOFED CS IS MOST COMMONLY ASSOCIATED WITH

LSVC

TOF CONSISTS OF


4

1. MALIGNMENT VSD


2. PS OR PA


3. OVERRIDING AO


4. RVH

RECORD ____ VELOCITY ACROSS ALL SHUNTS WITH _________

PEAK, CW

PERMANENT INCREASE IN PULM VASC RESISTANCE DUE TO PULMONARY ARTERIOLAR DAMAGE

EISENMENGERS SYNDROME

TRABEULAR VSD ARE ALSO CALLED _____.

MUSCULAR "THINK MUSCLES HAVE TRABECULATIONS"

RECORD_________VELOCITIES IF PEAK IS >_________

MEAN,


> 2 M/S



IN A CORONARY SINUS ASD, CONTRAST INJECTED INTO THE LEFT ARM WILL ENTER THE _____FIRST

LA

DOPP EXAM:


RECORD ______ FOR ALL 4 VALVES


NYQUIST=


(PW)

PEAK VELOCITIES

IN TOF VSD SHUNT IS USUALLY ____ TO ______=


________

RIGHT TO LEFT = CYANOTIC

IAA IS ASSOCIATED WITH _______SYNDROME

DIGEORGE

INLET VSDS ARE ALSO CALLED

ENDOCARDIAL CUSHION TYPE

PDA and A -V fistula are ________murmurs

continuous

MVP is common in

Marfan's syndrome

A downward displacement and deformity of the TV=

Ebstein's anomaly

Swiss cheese VSDs are usually __________

muscular

The close proximity of a __________VSD to the _______valve predispose the Ao to:

Supracristal Ao, Ai and sinus rupture

Failure of the endocardial cushion results in _______ VSD

inlet

A small VSD does not cause ________ or _______

dilation


increase flow

The most frequent lesion associated with sinus venosus ASD is ______

PAPVR usually right veins

a large VSD in a newborn won't initial dilate or increase flow because of

pulmonary vascular resistance is still high for 6 weeks

Failure of truncal swellings to spiral causes

transposition of the great vessels

Failure of endocardial cushions causes ________

AVSD

If the truncal valve fails to divide you get ___________

persistent truncus arteriosus

A _______ is always present in an interrupted arch

PDA

In MS there is an increased ______ wave = increased filling velocity

A wave

D TGA fix old school or special situations

Mustard Senning

If the heart folds to the _____ you get ______

levo-loop


or reversed ventricles

CC -TGA or L TGA the aorta is ____ and _____


the PA is _____ and ______

anterior and left



posterior and right

L TGA is also known is ____

congenitally corrected

Coronary sinus empties into the ________

right atrium

In L transposition ther is no ___ _____

MV to Ao continuity

the heart normally folds to the

right

Day 24 in depth

Bulboventricular loop because heart expands in restrictive pericardium

s3

Ventricular filling


(heart failure)

MVA

220/p1/2t

Rapid filling


2

1 av valves open


2 most filling occus

When all chordae insert in a single pap muscle=

parachute mitral valve

Parachute MV is in what syndrome

Shone's complex.

Cor triatriatum is caused by:

TAPVR to a confulence of LA

Obstruction of SVC casues

facial neck and scalp swelling

small ao valve, large PV R to L PDA=

IAA

PDA is _____ to ____ unless pulmonary hypertension is present

left to right

Rapid ejection


3

1 semilunar valves open


2 Ventricles contract


3 most of the ourflow occurs

an increase in oxygen typically closes the fetal _______

PDA

AI and PI are murmurs in what phase

Diastolic


Ducts stay open in


3

1 congenital rubella


2 maternal diabetes


3 downs syndrome

what are the consequences of l looping

ventricles are inverted

Map all shunts by

color

truncus arteriosus

Prostaglandin

Duct stays open

Inlet VSDs are common with ______ASD.

primum

Supracristal VSD is also called

suppulmonary

Compare RV (PA) pressure to _______

SBP

types of coarctation repairs


4

1 subclavian flap


2 Dacron/pericardial patch


3 end to end


4 balloon dilation stent

PW Doppler uses _______ ___________

range gating

At birth contractility increases due to


3

1 increases thyroid hormones


2 cortisol


3 catecholamines epi, nor epi

in PW _____________and ___________ can be adjusted = _______

time,


distance,


sample volume

A membranous VSD is also called_________

subaortic

Freidrich ataxia is associated with

HCM

IN CRITICAL STENOSIS THE LV EF ________ AND GRADIENTS DO NOT REFLECT THE TRUE SEVERITY

DECREASE

MILD AS


MOD AS


SEV AS

MILD< 40 MMHG


MOD 40-60 MMHG


SEV> 60 MMHG

PA BANDS ARE USED IN


2

DORV AND SINGLE VENTRICLES

TOF HAS ______MALALIGNMENT OF THE VSD

ANTERIOR

DILV IS AN

L TGA

LEFT SIDED EBSTEINS IS SEEN IN

L TGA

THE RV INFUNDIBULUM CAN BE OBSTRUCTED BY THE __________ LEAFLET IN EBSTEINS

ANTERIOR

IN TRUNCUS THERE IS A SINGLE SEMI LUNAR VALVE WITH UP TO _______LEAFLETS

5

PROSTAGLANDIN=


INDUCIN=





OPEN


CLOSE

IF THERE IS RV OUTFLOW TRACT GRADIENT OF PS THEN _____=________ PRESSURE

RV= PA PRESSURE

LA/AO RATIO BY M MODE SHOULD BE _______

<1.2

IN CALCULATING RV-RA GRADIENT FROM TR, USE_______MMHG IF LESS THAN 6 MONTH OLD

5 MMHG


IF GREATER THAN


SIX MONTHS OLD=10 MMHG

PRIMARY ECHOES HAVE ______ __________


REVERBERATIONS AND BLUR AND DEGRADE THE IMAGE

SIDE LOBES

___________FILTER OUT UNWANTED SIDE LOBES, REVERBERATIONS, NOISE AND CLUTTER

HARMONICS

WILLIAMS SYNDROME IS MOST LIKELY ASSOCIATED WITH_______

SUPRAVALVULAR AORTIC STENOSIS


ALSO OOS AND PS SUPRAVALVULAR

DORV IS ASSOCIATED WITH

DIGEORG SYNDROME


THINK DIDORV SYNDROME

BIG RV AND BIG CS

CARDIAC TYPE TAPVR

BLUE BABY AND BIG RV

TAPVR

RT TO LEFT SHUNT

QP


CYANOTIC QP/QS<1.0

AN OSTIUM PRIMUM ASD IS MOST COMMONLY ASSOCIATED WITH

CLEFT MV AND DOWNS SYNDROME

IN DORV A _____LIES BENEATH EACH SEMILUNAR VALVE

CONUS

RIGHT TO LEFT SHUNTS INCREASES THE Q OF QS OR QP?

QS

LEFT TO RIGHT SHUNT INCREASE THE Q______

QP

THE TENDON OF TODARO IS IN _______

KOCHS TRIANGLE

AVSD IS

ACYANOTIC

A PLSVC DRAINS TO __________

CORONARY SINUS

MOST COMMON VENOUS VARIANT

PERSISTENT LSVC

NOONAN's lesions

PV STENOSIS


DYSPLASTIC PV

AN ASD CAUSES OVERLOAD OF


2

RA RV

supravalvular ps is seen in

WILLIAMS SYNDROME AND


RUBELLA SYNDROME

SUBAORTIC, INFRACRISTAL,


MEMBRANOUS=

PERIMEMBRANOUS VSD

BLOOD FLOW IN ANOMALOUS LCA:

RCA TO LCA TO PA

A _______ IS NOT MANDATORY IN D TRANSPOSTION

PDA

D TGA REQUIRES A ___________AND __________

ASD,


PDA

SINUSOIDS ARE ASSOCIATED

PULMONARY ATRESIA


VENTRICULAR SEPTUM

D TGA= _______ GREAT VESSELS

PARALLEL

OBLIGATORY SHUNT FOR INTERRUPTED ARCH

RIGHT TO LEFT PDA


PULMONARY TO DESCENDING

ANOMALOUS RIGHT SUBCLAVIAN DOES NOT = _______

VASCULAR RING

CORAC GRADIENT 3 M/S


AS GRADIENT 2 M/S

20 MMHG

THE ______ ________ DIVIDES INTO THE LA AND RA


(FETAL)

PRIMITIVE ATRIUM

INNOMINATE ARTERY BRANCES INTO


2

RCC AND RSC

NOTE VALVULAR REGURGITATION BY _______ AND ________

CW AND COLOR

IN AN UNROOFED CORONARY SINUS, BLOOD FLOW FROM ____TO ________TO ________

LA TO CS TO RA

THE _______COURSES BETWEEN THE LEFT ATRIAL APPENDAGE AND THE MPA

LCA

HOLT ORAM TRAITS

NO THUMBS

VSD, MR AND TR ARE ALL _________ SYSTOLIC MURMURS

HOLO


(AKA PANSYSTOLIC)

THE FIRST EVENT IN CARDIAC DEVELOPMENT IS ____________

CARDIAC LOOPING

REDUCED EJECTION (2 THINGS)



1 SLOWER EMPTYING


2 AV VALVE LEAFLETS DRIFT TOWARD EACHOTHER

SHONE'S COMPLEX


5 (ANY THREE)

1 SUPRAVALVAR MITRAL RING


2 PARACHUTE MV


3 SUB AO MEMBRANE


4 BICUSPID AO VALVE


5 COARCTATION

CARDIAC INDEX

CO/ BSA


L/MIN/M2

A RIGHT AO ARCH IS COMMON IN _______

TOF

THE LCA TRAVELS BETWEEN THE ________ AND


_____________

LEFT ATRIAL APPENDAGE AND MPA

ASDs cause (2 THINGS)



RA AND RV VOLUME OVERLOAD,


PARADOXICAL SEPTAL MOTION

RECORD_________ AND ___________ VELOCITIES ACROSS SUB OR SUPRA VALVAR SENOSIS AND COARC

PEAK AND MEAN

LISTENING BEYOND A PW DISTANCE GIVES ERRORS

EXCEEDS NYQUIST LIMIT

AUTOGRAFT=


HOMOGRAFT=

SELF


ANOTHER HUMAN

LEFT OXYGEN SATS


RIGHT OXYGEN SATS

L 95-100%


R 70-80%

BECKER MD IS ASSOCIATED WITH

DILATED CM

8 TO 10% OF VSDs ARE

INLET

5-20% OF VSDs ARE

TRABECULAR

VSDs


inlet


trabecular


membranous


supracristal

inlet- endocardial cusshion


trabecular- muscular


membranous- sub aortic


supracristal - subpulmonary

what percent of all VSDs are______?


(most common)

80% are membranous

VSDs make up ______% of defects in hearts in kids?

20%

2-8% of VSDs are ________.


30% in Japan

Supracristal

Isovolumic ejection


3

1 increase pressure in ventricles


2 av valves close (all valves are now closed)


3 no volume change



These 3 things exacerbate HOCM


3

1 Tachycadia


2 dehydration


3 beta agonists

Contributes to the development of IVC, SVC, CS and RA

Sinus Venosus

The _____ portion of the ventricular septum forms from upward growth of the ventricular myocardium

muscular

contributes to the formation of Ao, PA and semilunar valves

Truncus arteriosus

Day 31

spiral septum=


division of Truncus into PA and Ao

The_______ portion of the ventricular septum forms from septation of bulbus

outflow

Day 20 in depth (3 THINGS)



1) Aortic arches PAs, carotid, duct


2) sinus venosus= IVC SVC CS


3)Cardiac loop= forms primative atrium vents, bulbus cordis

Ross-Kono procedure

PV to Ao


donor PV


resection of LVOT with patch enlargement

Homocystinuria is=

coarct

The most noticeable effect of a PDA is

left atrial enlargement

The ______ ________ crosses near where a PDA would be externally

Laryngeal nerve

A large PDA is usually durring the ____phase

Diastolic


Associated defects to D TGA

VSD ASD PS PDA

Supracardiac = cardinal veins =


(most common)

LSVC, RSVC, azygous


Bernoulli

4v2

Acyanotic Malformations (4 THINGS)



1 left to right shunts


2 Ventricular outflow obstructions (as coract)


3 ao arch abnormalities


4 Ventricular inflow obstructions

infracardiac=umbilic-vilelline=

portal vein

s2

av and pv closure


The AV node sits in the

Koch's triangle

If PVR is high, there may be little to no shunt in an _______ ________

AP window

Remember that laminar Doppler is_______ and turbulent flow is_________

hollow


filled in

TAPVR causes an RV __________ __________

volume overload

S-L-L


TRANSPO


L TGA

NORMAL ATRIA


INVERTED VENTRICLES


INVERTED GREAT ARTERIES

S-D-D


TRANSP


D TGA

NORMAL ATRIA


NORMAL VENTRICLES


AORTA TO RIGHT


IN TAPVR ALL TYPES HAVE A ______ TO _____


_________

RIGHT TO LEFT ASD

AN OSTIUM PRIMUM DEFECT IS WHEN THE ____ _______ FAILS TO CLOSE THE GAP

SEPTUM PRIMUM

FETAL SHUNTS


3

1 RIGHT TO LEFT PDA


2 RIGHT TO LEFT PFO


3 DUCTUS VENOSUS FROM PLACENTA

IN EBSTEINS THE ______ AND _____ LEAFLETS ARE DISPLACE INFERIORLY

SEPTAL AND POSTERIOR

IN EBSTEINS THE _________ LEAFLET IS SAIL-LIKE WITH ABNORMAL CHORDAE

ANTERIOR

FIRST BREATH


5

1 LUNGS EXPAND


2 PRESSURE FALLS


3 O2 LEVEL IN AO INCREASED


4 PDA CLOSES


5 INCREASED PULM BLOOD FLOW AND INCREASED LA PRESSURE= PFO

IN TAPVR 02 SATURATION ARE _______

EQUAL

IF THERE IS ONLY _________ UMBILICAL ARTERY, THEN THE ODDS ARE THERE IS CHD

ONE

IN TRUNCUS THERE IS NO ________

PULMONARY VALVE

THE CORONARY SINUS HAS THE ________ OXYGEN CONTENT IN THE WHOLE BODY

LOWEST

LARGE CORONARY SINUS ON PLAX IS SUSPICIOUS FOR

PERSISTENT LEFT SUPERIOR VENA CAVA

FAILURE TO SPIRAL LEADS TO

TGA

IN TOF AND TRUNCUS, MAKE SURE TO LOOK FOR _________ FROM THE DESC AO

COLLATERALS

IN HYPOPLASTIC LEFT HEART SYNDROME, THERE NEEDS TO BE A _________ TO _______ _________

LEFT to RIGHT ASD

TWO TYPES OF DORV

TOF TYPE


TRANSPOTYPE TAUSSIG BING

VISCERO ATRIAL SITUS


S


I


A

SOLITUS= NORMAL


INVERSUS= RIGHT ON LEFT


AMBIGUOUS= CAN'T TELL

IN HLHS FLOW IS _____TO GET TO CORONARIES

RETROGRADE

THE _____ALWAYS STICK WITH ABDOMINAL ORGANS

ATRIA

CALCULATING FS

LVIDD-LVIDS/


LVIDD

CALCULATE PEAK RV PRESSURE FROM CW

TR MAX+CVP

THE BULBUS CORDIS TURNS INTO THE ________

RV OUTFLOW TRACT

DOMING IN LONG AXIS MEANS THE VALVES

CURVE

COMPLETE VENTRICULAR SEPTATION REQUIRES FUSSION OF


3

1 ENDOCARDIAL CUSHION


2 MYOCARDIUM


3 BULBUS CORDIS



CATH/ MEAN GRADIENTS ARE

PEAK TO PEAK

TGA AORTIC VALVE AND RV LIE TO THE RIGHT

D TGA


CYANOTIC

THE ______PORTION OF THE VENTRICULAR SEPTUM FORMS FROM ENCOCARDIAL CUSHIONS

INLET

AS AND PS ARE _______SYSTOLIC

MID


AKA- CRESCENDO OR EJECTION MURMU

S4

ATRIAL CONTRACTION

T13 LESIONS


3

1 PDA


2 VSD


3 ASD


IN MS YOU CAN GET A _________ ______ ON THE VENTRICULAR WALL

JET LESION

CORONARY VEINS DRAIN TO THE __________

CORONARY SINUS

EISENMENGERS CAUSES ________

CYANOSIS

MALPOSED GREAT VESSELS


3

DORV


DOLV


SINGLE VENTRICLES



INCREASED PV RESISTANCE WOULD CAUSE ______ VSD FLOW

LESS

______IS ASSOCIATED WITH CLEFT MITRAL VALVE

OSTIUM PRIMUM ASD

THE PATHALOGICAL DETERIORATION OR WEAKENING OF CONNECTIVE TISSUE

MYXOMATOUS DEGENERATION

DIASTASIS

NOTHING HAPPENS


WAITING FOR ATRIAL CONTRACTION

Truncus type III

PAs lateral

CHARGE

C coloboma funny iris


H TOF, AVSD, ASD, VSD


A choanal atresia


R retarded growth


G genital small


E ear malformations

Pulmonary atresia

A superior mesenteric artery


B celiac axis


C abdominal aorta

Normal

L tga


Ao anterior and left


Pa Posterior and right

Mitral Artesia

D TGA


Ao anterior and rightward


PA posterior and leftward

Overriding tricuspid

MVP M MODE


Pan systolic hammocking

A svc


B innominate vein


C ao


D RPA


E LA


F pulmonary veins

1 central shunt


2 watersin-cooley


3 potts

VACTeRL

V vertebral anomalies


A implerfutate anus


C VSD, ASD, TET


Te tracheoedophageal fistula


R renal


L limb

Systolic


Diastolic


Atrial reversal

Ssn bifurcation

1RCCA


2 jv


3 RSCA

AV Concordance

Truncus arteriosus

Tricuspid atresia

MEMBRANOUS VSD SUB AORTIC


SUPRACRISTAL VSD SUB PULMONIC

Common AV valve

PAs posterior

Overriding mitral valve

A ao


B pa


C rupv


D rlpv


E la


F d ao


G lupv


H llpv

Single trunk

Normal

Situs

Ambiguous

AV discordance