RMW is a common complication of neuromuscular diseases. It causes a respiratory failure which may lead to death (Bourke, 2014). RMW can be classified as acute (as seen in Guillain-Barré syndrome), chronic and relapsing (relapse) (as seen in multiple sclerosis, myasthenia gravis), or relentlessly progressive (as seen in amyotrophic lateral sclerosis [ALS]) (Ambrosino, Carpene, & Gherardi, 2009; Areeyapinan & Phanthumchinda, 2010; Berrih-Aknin, Frenkian-Cuvelier, & Eymard, 2014). Assessment and diagnosis of RMW in neuromuscular subjects can be difficult and delayed and this because of the limb muscle weakness, which limits subjects from exceeding their limited ventilatory capacity (Laghi & Tobin, 2003).
Patients with NMD have a progressive inspiratory
Patients with NMD have a progressive inspiratory