Ucsf: Gi I Part 1

Front 1

what are the findings for Caroli's disease

Back 1

multifocal saccular dilatation of intrahepatic bile ducts that will appear as hypodense on ct and could have air-fluid levels

this could be several rounds or oval hypoidense cystic structures containing air fluid levels

Front 2

what is Caroli's disease associated with

3

Back 2

congenital hepatic fibrosis, medullary sponge disease, and autosomal recessive polycystic kidney disease

Front 3

what is the differential diagnosis of intrahepatic biliary cystic dilatation

3

Back 3

sclerosing cholangitis
choledochal cysT (Caroli's disease)
cholangiocarcinoma

Front 4

what is another name for a type III choledochal cyst

Back 4

choledochacele

Front 5

what number choledochal cyst is Caroli's disease

Back 5

5

Front 6

what is another name for mesenteric panniculitis
2

Back 6

mesenteric lipodystrophy, idiopathic retractile mesenteritis

Front 7

what are the imaging findings in mesenteric panniculitis

Back 7

irregular mesenteric mass central calcification and radiating desmoplastic reaction exhibiting fibrotic tenting of adjacent loops of small bowel

Front 8

what is a potential complication of mesenteric panniculitis

Back 8

small bowel obstruction

Front 9

can mesenteric panniculitis occur in the colon

Back 9

it more commonly occurs in the small bowel but it may occur in the colon

Front 10

what is the differential diagnosis for mesenteric panniculitis

Back 10

carcinoid tumor, or other neoplastic entity especially if there is a large fibrotic component

Front 11

when describing mesenteric panniculitis what does the word panniculitis imply

Back 11

there is a primary inflammatory component

Front 12

why is there different names for mesenteric panniculitis

Back 12

this is because the different names describe different parts of the pathological process result in fibro-fatty thickening of the mesenteric

Front 13

what does mesenteric lipodystrophy imply about mesenteric panniculitis

Back 13

the word lipodystrophy is used when fatty degeneration predominates

Front 14

when is retractile mesenteritis used to describe mesenteric panniculitis

Back 14

this is one the predominate component is fibrosis

Front 15

what are the most common causes of mesenteric panniculitis
3

Back 15

most commonly idiopathic, infection, foreign bodies

Front 16

what is pancreatic lipomatosis

Back 16

this is fatty replacement of the pancreas

Front 17

is pancreatic lipomatosis common

Back 17

yes and there is increased incidence what age

Front 18

what is the differential diagnosis of pancreatic lipomatosis

3

Back 18

pure pancreatic atrophy, congenital pancreatic hypoplasia, previous pancreatic resection

Front 19

what are two causes of pure pancreatic atrophy

Back 19

chronic pancreatitis, cystic fibrosis

Front 20

what is a syndrome in which congenital pancreatic hyperplasia may occur

Back 20

schwachman syndrome

Front 21

what is the second most common primary hepatic tumor

Back 21

after hepatocellular carcinoma cholangiocarcinoma is the second most common primary hepatic tumor

Front 22

what are some risk factors for cholangiocarcinoma
5

Back 22

choledochal cyst
ulcerative colitis
Caroli's disease
Clonorchis
primary sclerosing cholangitis

Front 23

what is the klatskin tumor

Back 23

this is a tumor located at the bifurcation of the Main biliary ducts

Front 24

how could you differentiate cholangiocarcinoma from hepatocellular carcinoma on post contrast imaging

Back 24

cholangiocarcinoma is typically have delayed enhancement whereas hepatocellular carcinoma is tend to have great is attenuation in the arterial phase

Front 25

name three features of cholangiocarcinoma's on CT

Back 25

large, hypo attenuating, a regular margins

Front 26

what is the differential diagnosis of cholangiocarcinoma

3

Back 26

metastasis, hepatocellular carcinoma, sarcoma

Front 27

what are two other names for splenic hamartomas

Back 27

Splenomas, nodular hyperplasia of the spleen

Front 28

what are the CT characteristics of a splenic hamartoma

Back 28

this is hyperintense in the arterial phase and I so dense to the splenic parenchyma on the non-contrast and portal venous phase

Front 29

can a splenic hamartoma have hypointense areas

Back 29

yes, these represent cystic components or necrosis

Front 30

what are splenic hamartoma is associated with

Back 30

tuberous sclerosis

Front 31

name some malignant splenic tumors

3

Back 31

lymphoma, mucinous cyst adenocarcinoma, metastasis

Front 32

what is a potential complication of the splenic hamartoma

Back 32

splenic rupture

Front 33

what is the differential diagnosis to splenic mass

5

Back 33

cavernous hemangioma, splenic hamartoma, hemangioendothlioma, malignant fibrosis histiocytoma, inflammatory pseudo-tumor

Front 34

what does juvenile polyposis look like on CT

Back 34

there are multiple large lobulated filling defects within the colon

Front 35

what is the inheritance pattern of juvenile polyposis

Back 35

autosomal dominant

Front 36

is there risk of malignant transformation but juvenile polyposis

Back 36

yes, 9 to 50%

Front 37

what is the associated cancer to juvenile polyposis

Back 37

colon cancer is the most common but gastric cancer and pancreatic cancer may occur

Front 38

what is the most common presentation of juvenile polyposis

Back 38

G.I. bleeding

Front 39

what are some causes of hamartomtous polyps in the G.I. tract?
2

Back 39

Cowden (multiple hamartoma syndrome)

Peutz-Jeghers syndrome

Front 40

what other cancers are associated with Cowden syndrome
2

Back 40

breast and thyroid cancer

Front 41

what cutaneous feature is associated with peutz jeghers syndrome

Back 41

mucocutaneous hyperpigmentation

Front 42

where is the most common location of the hamartomatous polyps of peutz jeghers syndrome

Back 42

the stomach

Front 43

what are some causes of adenomatous polyps
3

Back 43

familial polyposis coli, turcots syndrome, gardeners syndrome

Front 44

what kind of tumors is turcots syndrome associated with

Back 44

brain tumors; glioblastomultiforme and medulloblastoma

Front 45

what is associated with gardeners syndrome
3

Back 45

colonic polyps, osteomas, soft tissue tumors

Front 46

what cutaneous feature is associated with peutz jeghers syndrome

Back 46

mucocutaneous hyperpigmentation

Front 47

where is the most common location of the hamartomatous polyps of peutz jeghers syndrome

Back 47

the stomach

Front 48

what are some causes of adenomatous polyps
3

Back 48

familial polyposis coli, turcots syndrome, gardeners syndrome

Front 49

what kind of tumors is turcots syndrome associated with

Back 49

brain tumors; glioblastomultiforme and medulloblastoma

Front 50

what is associated with gardeners syndrome
3

Back 50

colonic polyps, osteomas

Front 51

what what is the location of osteomas that typically occur in with gardeners syndrome

Back 51

frontal sinus, and the mandible

Front 52

what kind of soft tissue tumors are associated with gardeners syndrome

Back 52

dismally tumors, epidermoid inclusion cyst, fibroma, lipoma, leiomyoma

Front 53

what are some conditions that cause juvenile polyps

Back 53

juvenile polyposis, cronkite-canada