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11 Cards in this Set
- Front
- Back
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21.Tx of CVID?
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a. Infusion of IV immunoglobulins.
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22.Presentation of X-linked Agammaglobulinemia (Bruton’s)?
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a. MALE child w/recurrent sinopulmonary infections.
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23.Diagnostic testing for x-linked agammaglobulinemia (Bruton’s)?
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a. Lymph nodes, adenoids, and the spleen are diminished in size or absent.
b. B cells are missing, as are the immunoglobulins! |
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24.Tx of Bruton’s X-linked agammaglobulinemia?
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a. Like CVID, X-linked agammaglobulinemia is treated w/infusions of IVIG.
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25.IgA deficiency?
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a. Most common primary immunodeficiency.
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26.Presentation of IgA deficiency?
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a. Many people are asymptomatic.
b. Some have recurrent sinopulmonary infections. c. There is also a spruelike malabsorption syndrome as well as an increased incidence of atopic conditions. d. Some people present w/anaphylaxis when receiving blood from donors who are not IgA deficient. |
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27.Tx of IgA deficiency?
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a. Treat the infections as they arise.
b. IVIG will not work since it has little IgA in it. |
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28.Hyper IgE syndrome Presentation?
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a. Recurrent skin infections caused by staph.
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29.Tx of Hyper IgE syndrome?
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a. Tx the infections as they arise.
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30.A 3 yo boy comes in w/recurrent sinopulmonary infections. There are no nodes palpated in the cervical area and no tonsils seen on oral exam. The child has been treated for an infection every 1-2 months since birth. There are not skin infections. What is the most likely diagnosis?
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a. X-linked agammaglobulinemia.
b. It is seen exclusively in male children, whereas CVID presents in adults. c. The absence of skin infection in this case goes strongly against hyper IgE syndrome. These pts are best managed with IVIG infusions on a regular basis and w/abx for infections as episodes arise. |
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31. Complete
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31. Complete
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