Oral Path Exam 3 Chapter 6

Front 1

Is a autosomal recessive condition manifesting as marked destruction of the periodontal tissue and palmar- plantar hyperkeratosis

Back 1

Papillon Lefevre

Front 2

Has a autosomal Dominate inheritance pattern. The syndrome manifests as osteomas, multiple odontomas, and intestinal polyps that can become malignant after the age of 30.

Back 2

Gardners Syndrome

Front 3

The pulp chambers and root canal are severely narrowed or entirely lost to radiographic identification in the autosomal domination condition____?

Back 3

Dentinogenesis imperfecta type II

Front 4

Prolonged retention of primary teeth is most often found in children with

Back 4

Cliedocranial dysplasia

Front 5

Is a rare disturbance of dentin formation characterized by normal enamel, pulpal obliteration, defective root formation, a tendency toward multiple perical radiolucencies, and early exfoliation.

Back 5

Radicular Dysplasia

Front 6

The hereditary dental defect in which the enamel of the teeth is soft and under calcified in context but normal in quality is

Back 6

Enamel Hypocalcification

Front 7

is a disturbance of development characterized primarily by brittle bones and is associated with blue sclera and deafness.

Back 7

Osteogenesis Imperfecta

Front 8

Is a benign, hereditary, painless bilateral swelling of the jaws. Mandible is most common, Often a delayed eruption of the permanent dentition.

Back 8

Cherbuism

Front 9

A child with fine, sparse hair, that lacks sweat glands. Radiographs reveal no tooth buds of either dentition.

Back 9

Ectodermal Dysplasia

Front 10

Autosomal dominate condition characterized by multiple neurofibromas. 3-15 % may undergo malignant transformation. Cafe au lait skin pigmentation may also be seen

Back 10

Von Recklinghausen

Front 11

autosomal dominant disorder characterized by multiple intestinal polps and multiple melanotic macular pigmentations of the skin and mucosa

Back 11

Peutz Jegher's

Front 12

Autosomal dominate condition marked by mild hypertension. Oral manifestations include multiple cysts of the jaws (odontogenic keratocysts) which will recur also bifurcated ribs are present.

Back 12

Nevoid Basal Cell Carcinoma

Front 13

MEN 2B is a autosomal dominante syndrome involving a combination of three disorders ____, ____, and _____. Why is early diagnosis of this disorder important?

Back 13

Multiple mucosal neuromas, medullary carcinomas of thyroid gland, and pheochromocytoma.
Early diagnosis bc the high malignant potential of thyroid carcinoma.

Front 14

A patient with ______ is at risk of dying from aortic aneurism. Antibiotics before dental tx would be needed.

Back 14

Marfan Syndrome

Front 15

Autosomal Dominate condition features hypoplasia or absence of zygomatic bones, a fishlike mouth, open bite and deafness.

Back 15

Mandibulofacial Dysotosis