Study your flashcards anywhere!

Download the official Cram app for free >

  • Shuffle
    Toggle On
    Toggle Off
  • Alphabetize
    Toggle On
    Toggle Off
  • Front First
    Toggle On
    Toggle Off
  • Both Sides
    Toggle On
    Toggle Off
  • Read
    Toggle On
    Toggle Off
Reading...
Front

How to study your flashcards.

Right/Left arrow keys: Navigate between flashcards.right arrow keyleft arrow key

Up/Down arrow keys: Flip the card between the front and back.down keyup key

H key: Show hint (3rd side).h key

A key: Read text to speech.a key

image

Play button

image

Play button

image

Progress

1/27

Click to flip

27 Cards in this Set

  • Front
  • Back
CYSTIC FIBROSIS
-INHERITED D/O
-CAUSES DISFUNCTION IN ALL EXOCRINE GLANDS
-MOST COMMON INHERITED DISEASE IN CHILDREN (CAUCASIONS)
-AUTOSOMAL RECESSIVE TRAIT:BOTH PARENTS MUST BE CARRIERS
-2 PARENTS CARRIERS=25 PERCENT CHANCE THAT CHILD WILL HAVE CF
WHAT GIVES RISE TO SEVERAL SEEMINGLY UNRELATED CLINICAL FEATURES AS A RESULT OF DYSFUNCTION OF THE EXOCRINE GLANDS
-A GENETIC DEFECT OF CHROMOSOME 7
WHAT SYSTEMS ARE AFFECTED WITH CF
-LUNGS
-GI
-**PANCREAS
WHAT IS CF CHARACTERIZED BY
INCREASED PERSPIRATION
-SWEAT HAS UP TO 5X'S AS MUCH SALT TO IT "TASTE SALTY WHEN KISSED"
PULMONARY EFFECTS
-PRESENT IN MOST CHILDREN WITH CF
-PULMONARY COMPLICATIONS ARE MOST SERIOUS(MAY CAUSE DEATH)
-VISCOUS MUCOUS COLLECTS IN THE SMALL AIRWAYS (BRONCHIOLES)
WHAT DOES THE VISCOUS MUCOUS IN THE AIRWAY CAUSE
-OBSTRUCTION TO AIRFLOW-->HYPOXIA,HYPERCAPNIA,ACIDOSIS
-AIR TRAPPING
-ATELECTASIS
-STAGNATION OF SECRETIONS
-CYANOSIS,CLUBBING OF NAILS
-MUCOUS SO THICK,CANNOT EXPECTORATE
-S/S SIMILAR TO COPD
WHAT RESULTS AFTER PANCREAS AFFECTED BY CF
**MALABSORPTION**
-STETORRHEA(FREQUENT,LARGE,LOOSE,FOUL SMELLING,GREASY STOOLS)
-PANCREATIC ENZYMES (AMYLASE,TRYPSIN,LIPASE)ARENT AVAILABLE TO BREAK DOWN FATS,CHO,PROT.
WHAT SYSTEM IS AFFECTED DURING THE LATE STAGES OF SEVERE DISEASE (DIABETES MELLITUS)
-ISLETS OF LANGERHANS
WHAT OCCURS WHEN ISLETS OF LANGERHANS AFFECTED
-BOWEL OBSTRUCTION (FROM THICK MECONIUM) OR RECTAL PROLAPSE IN CHILD
-OBSTRUCTION OF BILIARY DUCTS FROM MUCOUS (CAUSES CIRRHOSIS AND PORTAL HYPERTENSION)
-ANEMIA OF CHRONIC DISEASE
SYMPTOMS OF MALABSORPTION
-FAILURE TO THRIVE
-FREQUENT FROTHY,FOUL SMELLING GREASY STOOLS-**STETORRHEA
-WT LOSS DESPITE VORACIOUS APPETITE
-SALTY TASTE TO SWEAT
WHAT IS CF MISTAKEN FOR
-WHOOPING COUGH,CHRONIC BRONCHITIS,ASTHMA
WHY MIGHT WOMEN WITH CF HAVE DELAYED SEXUAL MATURATION
INFERTILITY IN WOMEN DUE TO THICKENED VAGINAL MUCOUS
-MALES HAVE ATROPHIED OR OBLITERATED VAS DEFERENS
WHAT IS THE DEFINITIVE DIAGNOSTIC TEST FOR CF
THE SWEAT TEST
PULMONARY S/S
-TACHYPNEA,WHEEZING
-CHRONIC PRODUCTIVE
-DYSPNEA
-BARREL CHEST
-CLUBBING AT NAIL BEDS FROM HYPOXIA
-CYANOSIS
G.I. S/S OF CF
-FAILURE TO THRIVE
-NEWBORN=MECONIUM ILEUS (THICK MECONIUM CAUSING AN INTESTINAL OBSTRUCTION)
THE SWEAT TEST
-SAFE AND RELIABLE IF DONE AT MED CTR
-MEASURES SODIUM AND CHLORIDE IN SWEAT
-SIBLINGS OF CHILD W/ CF SHOULD ALSO BE TESTED
-AFTER PUBERTY RESULTS MORE DIFFICULT TO INTERPRET
NORMAL SODIUM CONCENTRATION=
POSITIVE SWEAT TEST=
NORMAL SODIUM<40 MEQ/L
POSITIVE SWEAT TEST>60 MEQ/L
PANCREATIC ENZYMES
OBTAIN SPECIMEN BY GASTROSCOPY
-DECREASED OR ABSENT LEVELS SEEN WITH CF
FAT ABSORPTION IN STOOLS
5 DAY COLLECTION
NURSING DIAGNOSIS
-INEFFECTIVE AIRWAY CLEARANCE
-ALTERATION IN NUTRITION
-KNOWLEGE DEFICIT
WHAT IS THE FUTURE THERAPY FOR CF
GENE THERAPY
AMILORIDE
NEW DRUG**
WORKS BY AEROSOL TO THIN RESPIRATORY MUCOUS
-USED IN ALL PT'S WITH CF AND PULMONARY SYMPTOMS
PULMOZYME (DORMASE)
THINS SECRETIONS
-IBUPROFEN IN HIGH DOSES DECREASES RATE OF LUNG INFLAMMATION
WHAT TO DO FOR PULMONARY
-EXPECTORANTS (IODIDES)
-BREATHING EXERCISES BID
-POSTURAL DRAINAGE
-HUMIDITY (AEROSOL OR NEBULIZATION)
-INCREASE ORAL FLUIDS
-ANTIBIOTICS
WHAT TO DO FOR PANCREATIC
ADMINISTER PANCREATIC ENZYMES WITH MEALS AND SNACKS TO OBTAIN NORMAL BOWEL MOVEMENT AND GROWTH
-PANCREASE,COTAZYM-S
DIETARY MANAGEMENT FOR CF
NEEDS TO EAT MORE THAN NORMAL CHILD
-HIGH PROTEIN,HIGH CALORIE,HIGH SALT
-MODERATE FAT
-REPLACEMENT OF VIT A,D,E,K
LIFE EXPECTANCY FOR CF
30 YRS