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19 Cards in this Set

  • Front
  • Back
PROPHYLACTIC THERAPY IS USED TO__
-STARTED AT AGE__
-FACTOR GIVEN__
TO KEEP FACTOR LEVEL > 1
-START AT AGE 1-2 YRS
-FACTOR VIII TIW
-FACTOR IX BIW
-IVAD
PT SHOULD BE VACCINATED AGAINST__
1.HEPATITIS B
2.PT STILL AT RISK FOR HEP C
OTHER NSG MEASURES FOR HEMOPHILIA
-NO IM (ONLY SUB Q)
-GOOD DENTAL CARE
-CHECK TYPE OF SHOES
-MED ALERT ID
1.COSTLY DISEASE
2.NEED COMPREHENSIVE TEAM APPROACH
3.GENETIC COUNSELING
4.GENE THERAPY IN PROCESS
5.PROPHYLACTIC THERAPY
NSG PLAN/IMPLEMENT FOR HEMOPHILIA
A.GROWTH AND DEVELOPMENT
-AVOID OVERPROTECTING
-ALLOW CHILD TO RUN,EXPLORE,CLIMB
-NEED REGULAR PROGRAM OF EXERCISE,SELF ESTEEM
B.BLEEDING EPISODE
-ADMINISTER**FACTOR A OR B CONCENTRATE IV (AHF=ANTIHEMOPHILIC FACTOR)
-(9-12 YRS OLD=SELF ADMINISTRATION)
-**CRYOPRECIPITATE NO LONGER RECOMMEND
NURSING FOR MINOR CUT
TREAT SAME AS WOULD FOR ANYONE ELSE
-APPLY PRESSURE Q 10-15 MIN
-INCREASE EXTREMITY
-IMMOBILIZE
-COLD PACKS
NSG DIAGNOSIS FOR HEMOPHILIA
1.RISK FOR INJURY
2.KNOWLEDGE DEFICIT
3.INEFFECTIVE COPING
LAB TEST
1.STAGE 1 (PTT)
CHECK HEPARIN
2.STAGE 2 (PT)
CHECK COUMADIN
FACTOR ASSAY PROCEDURE
IF HEMOPHILIA MILD,DIAGNOSE__
DELAYED, POST-OP
IF HEMOPHILIA SEVERE,DIAGNOSIS MADE DURING __
INFANT/TODDLER
ASSESSMENT
HISTORY
P.E.
HISTORY-HEMOPHILIA IS A GENETIC D/O
FAMILY HISTORY
HISTORY OF PROLONGED BLEEDING
P.E.:1.VS,SKIN COLOR,TEMP,DYSPNEA
2.JOINT SWELLING
3.BRUISES
MAJOR CONCERN
HEMARTHROSIS(BLEEDING IN THE JOINTS)
S/S:TINGLING,BUBBLING SENSATION,CAN BE SPONTANEOUS JOILT TWIST
-JOINT WILL BE DAMAGED AND SURGERY NEEDED.JOINT WILL SWELL W/BLD AND GET STIFF.TISSUE WILL BE DESTROYED-->ANKYLOSIS
HEMARTHROSIS CAN LEAD TO__
ANKYLOSIS
SEVERITY OF HEMOPHILIA DEPENDENT ON__
AMT OF FACTOR PRESENT
CHRISTMAS DISEASE
FACTOR IX IS DEFICIENT
AKA: HEMOPHILIA B
-AFFECTS 2ND PHASE OF 1ST STAGE IN COAGULATION PROCESS(THROMBOPLASTIN)
WHAT SHOULD PT BE CONCERNED W/ HEMOPHILIA
INTERNAL BLEEDING
WHAT HAPPENS TO BLEEDING W/ HEMOPHILIA
BLEEDING IS PROLONGED
WHY?BECAUSE NO CLOTTING FACTOR
NOT:EXCESSIVE BLEEDING,NOT PROFUSE BLEEDING,NOT FASTER BLEEDING
CLASSIC HEMOPHILIA
FACOR VIII IS DEFICIENT
AKA: HEMOPHILIA A
VON WILLEBRAND
MALE AND FEMALE
HEMOPHILIA
INHERITED D/O OF BLOOD CLOTTING
- X LINKED RECESSIVE=MALE
- CARRIERS FEMALE=ASYMPTOMATIC