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22 Cards in this Set
- Front
- Back
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What can be seen on PE in Allergic Rhinitis?
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Boggy, edematous, blue, & pale nasal passages
Nasal Salute Nasal crease Allergic shiners |
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What may a nasal smear of patients with allergic rhinitis show?
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Eosinophils
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Hives, are red raised skin lesions of various sies that may be localized or generalized = ?
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Urticaria
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How does Angioedema differ from Urticaria?
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lesions appear to be in deeper layers of skin, subcutaneous, or other tissues are involved
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Inflammatory skin disorder characterized by erythema, edema, pruritis, exudation, crusting, & scaling
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Atopic Dermatitis = Eczema
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What are the treatments for Atopic Dermatitis?
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-bathing LESS FREQUENTLY & using BATH OILS
-avoid extremes in temp's -wear smooth-textured clothes & avoid WOOL -Antihistamines for itching -TOPICAL CORTICOSTEROIDS |
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A 15-month old child presents to the physician with fever of 39 C. On physical exam the pt is noted to have a right tympanic membrane that is erythematous & bulging & that has obscure landmarks & no mobility. On review of the medical record you note that since 9 months of age this pt has had multiple infections w/ Otitis media, sinusitis, & pneumonia
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X-linked Agammaglobulinemia
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What is the definition of X-linked Agammaglobulinemia?
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severe hypogammaglobulinemia caused by defects in B lymphocytes
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How do pts with Bruton's present?
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after maternal Ab's fall at about age 6-12 months
Susceptible to repeated infections such as pneumonias, persistent otitis media, & sinusitis PE may show hypoplasia of tonsils & adenoids. There is no LAD or Splenomegaly |
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When should Bruton's diagnosis be considered?
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in pts with extremely low levels of IgG, IgA, IgM, & IgE & in the absence of circulating B cells
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A 3 yo child is brought to your office b/c of recurrent URI's & recurrent UTI's, as well as chronic diarrhea
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IgA deficiency
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What is IgA deficiency associated with?
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SLE & RA as well as increased incidence of CA
One must also be careful when administering blood & blood products to pts with IgA deficiency |
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A 3 week old infant presents with a generalized seizure. The patient was born to a 22 yo white woman, G1P1, full term, via SVD. Mother had good prenatal care & denies tobacco, drugs, & alcohol. There were no complications at delivery. The patient weighed 7 lb 6 oz at birth and has gained weight. The infant has been feeding & sleeping well. On physical exam the pt has hypertelorism, low-set ears, micrognathia, & a fish mouth
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DiGeorge Syndrome
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Define DiGeorge Syndrome
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Hypoplasia of the THYMUS & PARATHYROIDS due to 3rd/4th Pharyngeal Pouch dysfunction
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What are some "other" features of DiGeorge Syndrome?
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-Congenital Heart Disease
-Hypertelorism = Abnormal distance between two paired organs. -Esophageal atresia -Bifid uvula -Micrognathia = small jaw |
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What is the etiology of DiGeorge Syndrome?
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microdeletions of specific DNA sequences from chromosome 22qll.2
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How do babies with DiGeorge Syndrome present?
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Hypocalcemic seizure
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A 1 year old infant presents to his physician with severe eczema. On physical exam the pt is noted to have draining ears as well as a petechial rash. Review of the medical record reveals that the pt has recurrent infections, including otitis media & pneumonia
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Wiskott-Aldrich Syndrome
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What is the definition of Wiskott-Aldrich syndrome?
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X-linked recessive disese w/:
1. recurrent infections 2. Thrombocytopenia = petechiae 3. Eczema |
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What diagnostic tests help to diagnose Wiscott-Aldrich syndrome?
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IgA & IgE are elevated
IgM is low |
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What is the treatment for Wiskott-Aldrich Syndrome?
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Splenectomy may correct Thrombocytopenia
BMT is treatment & cure |
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How does a child with Ataxia-telangiectasia present?
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-Cerebellar ataxia
-hx of recurrent Sinopulmonary disease -Masklike facies w/ drooling, tics, & irregular eye movements |
