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13 Cards in this Set

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Transient Hypoglobulinemia
Causes:
Delay of IgG production
Possibly genetic
Manifestations:
Increase in pyogenic (pus forming) infections

Transient (disappears by age 4)
X-Linked Hypogammaglobulinemia
Cause:
Genetic
Manifestations:
Significant problem with infections caused by encapsulated bacteria
Common Variable Immunodeficiency
Cause:
Genetic
Manifestations:
Enlarged tonsils & nodes
Recurrent infections
IgG Subclass Deficiency
Cause:
Genetic
Manifestations:
Recurrent infections
DiGeorge Syndrome
Causes:
Embryonic developmental defect

Teratogens
Manifestations:
Head, neck and heart defects
Hypocalcemia
Tetanus (within 24 hours of birth)
Recurrent infections
X-Linked Immunodeficiency with Hyper IgM
Cause:
Genetic
Manifestations:
Pyogenic infections
Combined Immunodeficiency Disorder
Cause:
Genetic
Manifestations:
Ataxia: motor dysfunction
Telangiectasia: vasodilation
Failure to thrive
Chronic infections
Chronic diarrhea
Sepsis
Severe Combined Immunodeficiency Disorder (SCIDs)
Cause:
Genetic
Manifestations:
Ataxia: motor dysfunction
Telangiectasia: vasodilation
Failure to thrive
Chronic infections
Chronic diarrhea
Sepsis
Complement Dysfunction
Causes:
Primary: decrease of complement proteins (C1 thru C9)

Secondary: hepatic failure and autoimmune disease
Manifestations:
Vasculitis
Edema
Nausea
Vomiting
Diarrhea
Chronic Granulomatous Disease
Cause:
Genetic
Manifestations:
Recurrent infections
Granulomatous lesions
Chediak-Higashi Syndrome
Cause:
Genetic
Manifestations:
Giant granules
Bleeding
Partial albinism
Peripheral neuropathy
Lymphoma
Host vs Graft
Causes:
Hyperacute: immediate
Acute: days
Chronic: months
Manifestation:
Organ rejection
Graft vs Host
Causes:
Acute: days
Chronic: months

Immune competent cells are transplanted into immune compromised host
Manifestations:
Pruritic rash
Desquamation
Nausea
Bloody diarrhea
Death