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13 Cards in this Set
- Front
- Back
- 3rd side (hint)
Transient Hypoglobulinemia
|
Causes:
Delay of IgG production Possibly genetic |
Manifestations:
Increase in pyogenic (pus forming) infections Transient (disappears by age 4) |
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X-Linked Hypogammaglobulinemia
|
Cause:
Genetic |
Manifestations:
Significant problem with infections caused by encapsulated bacteria |
|
Common Variable Immunodeficiency
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Cause:
Genetic |
Manifestations:
Enlarged tonsils & nodes Recurrent infections |
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IgG Subclass Deficiency
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Cause:
Genetic |
Manifestations:
Recurrent infections |
|
DiGeorge Syndrome
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Causes:
Embryonic developmental defect Teratogens |
Manifestations:
Head, neck and heart defects Hypocalcemia Tetanus (within 24 hours of birth) Recurrent infections |
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X-Linked Immunodeficiency with Hyper IgM
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Cause:
Genetic |
Manifestations:
Pyogenic infections |
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Combined Immunodeficiency Disorder
|
Cause:
Genetic |
Manifestations:
Ataxia: motor dysfunction Telangiectasia: vasodilation Failure to thrive Chronic infections Chronic diarrhea Sepsis |
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Severe Combined Immunodeficiency Disorder (SCIDs)
|
Cause:
Genetic |
Manifestations:
Ataxia: motor dysfunction Telangiectasia: vasodilation Failure to thrive Chronic infections Chronic diarrhea Sepsis |
|
Complement Dysfunction
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Causes:
Primary: decrease of complement proteins (C1 thru C9) Secondary: hepatic failure and autoimmune disease |
Manifestations:
Vasculitis Edema Nausea Vomiting Diarrhea |
|
Chronic Granulomatous Disease
|
Cause:
Genetic |
Manifestations:
Recurrent infections Granulomatous lesions |
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Chediak-Higashi Syndrome
|
Cause:
Genetic |
Manifestations:
Giant granules Bleeding Partial albinism Peripheral neuropathy Lymphoma |
|
Host vs Graft
|
Causes:
Hyperacute: immediate Acute: days Chronic: months |
Manifestation:
Organ rejection |
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Graft vs Host
|
Causes:
Acute: days Chronic: months Immune competent cells are transplanted into immune compromised host |
Manifestations:
Pruritic rash Desquamation Nausea Bloody diarrhea Death |