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33 Cards in this Set
- Front
- Back
- 3rd side (hint)
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What is cystic fibrosis? |
Lungs pancreas liver intestine Thick mucus Loss of pulmonary and respiratory function |
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Tx for lung complications |
Bronchodilator open Hypertonic saline mobilize Dornase Alfa thin Chest physio move Inhaled antibiotic control infection PO azithromycin reduce inflammation and pseudomonas biofilm Transplant |
BS DC aat |
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Pseudomonas infection? |
Two IV drugs recommended |
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When is inhaled antibiotics recommended |
Chronic pseudomonas a. Cycle with 28 days therapy |
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Pulmozyme |
Dornase Alfa |
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Dornase Alfa storage |
Ampules in ref Protect from light |
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Bethkis |
Tobramycin inh soln |
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Kitabis pak |
Tobramycin inh soln |
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Tobramycin se |
Ototoxicity, tinnitus, voice alter, dizziness, bronchospasms, mouth/throat pain |
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Tobramycin dose ___ apart |
6 |
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Tobramycin inh soln storage |
Recommend refrigerate Room temp 28 days |
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Tobi podhaler |
Tobramycin inh powder |
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Tobramycin inh powder storage dose |
6 h apart Don't swallow capsule Room temp Use with podhaler |
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Cayston |
Aztreonam inh soln |
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Azactam |
Aztreonam IV |
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Aztreonam se |
Allergic rxn, bronchospasm, fever, wheezing, cough, chest discomfort |
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Aztreonam dose storage |
4h apart Reconstitute with sterile diluent give immediately Recommend ref, room temp 28 days |
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Malabsorption tx |
Fat dense diet Pancreatic enzyme replacement PPIs Vitamin adek Insulin |
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Pancrelipase is combo of |
Lipase Amylase Protease |
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How to adjust pancrelipase |
Adjust q3-4 days until stools normalize Not more than 6000units/kg/meal |
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When to give pancrelipase |
Prior to meals 50% mealtime dose given with snacks High fat content need higher doses |
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Pancrelipase max |
Lipase <= 2500 units/kg/meal <=10000 units/kg/day |
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Viokace is ___ and needs.. |
Not enteric coated, needs to be given with PPI |
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Pancrelipase se |
Mucosal irritation Abdominal pain, flatulence, nausea |
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Pancrelipase storage |
Doesn't need ref Don't chew/crush |
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Ivafactor indication |
>= 2y/o have cftr Gene mutation |
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Orkambi indication |
>= 6y/o homozygous f508 mutation cftr gene |
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Kalydeco |
Ivacaftor |
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Orkambi |
Ivafactor Lumacaftor |
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Cystic fibrosis transmembrane conductance regulator potentiator dosing |
With high fat containing food |
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Tobi podhaler how many capsules at once |
4 |
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Pancrelipase can be sprinkled on.. |
Soft food applesauce, banana, pears. Use immediately |
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Creon, lio-prot-amyl, pancreaze, pertzye, ultresa, viokace, zenpep |
Pancrelipase |
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