Reading...
Play button
Play button
Use LEFT and RIGHT arrow keys to navigate between flashcards;
Use UP and DOWN arrow keys to flip the card;
H to show hint;
A reads text to speech;
22 Cards in this Set
- Front
- Back
|
Avg Life Span of a Cystic Fibrosis pt?
|
37.4 years
|
|
|
What PFT is affected in Cystic Fibrosis?
|
FEV1 is decreased
|
|
|
Race and CF?
|
Its all about the white people
Others get it, just not often |
|
|
Location of CF gene?
|
Long arm of 7
|
|
|
Inheritance pattern of CF?
|
Auto Recessive
|
|
|
why is some pts' CF worse than others?
|
CFTR gene is big
There are lots of different mutations that can lead to lots of different CF manifestations |
|
|
Which mutation is bad bad?
|
delta-F508
|
|
|
Which is the most feared infection that can complicate CF?
|
B. cepacia
|
|
|
what is anasarca?
|
body swelling from protein malnutrition
|
|
|
Typical male-specific CF symptom?
|
Infertility from absent Vas Deferens
|
|
|
Frequency of male infertility in CF pts?
|
~90%
|
|
|
% of CF pts w/ a normal sweat test?
|
1%
|
|
|
What infection is a red flag for additional CF testing?
|
Pseudomonas
|
|
|
What does CF look like on a flow-volume curve?
|
Obstructive disease
|
|
|
What are the majority of CF deaths attributed to?
|
Resp Failure or Pneumonia
|
|
|
Area of lungs more predominantly affected in CF?
|
Central area more than periphery
|
|
|
Appearance of Liver?
|
shrunken, irregular borders
|
|
|
Appearance of pancreas in CF?
|
can be mostly replaced by fat
|
|
|
Drugs that can help CF pts?
|
Pulmozyme
Tobi? Azithromycin |
|
|
Mechanism of Pulmozyme?
|
Decreased Inflammatory Response by decreasing viscous mucus
|
|
|
Nutrition in CF pts?
|
High fat
High protein high Calories |
|
|
How are lung transplants special in CF pts?
|
they're double transplants b/c if you left one lung, it'd still get infected
|
